3.Song Y, et al. Reduced Intensity Conditioning Followed by Allogeneic Hematopoietic Stem Cell Transplantation Is a Good Choice for Acute Myeloid Leukemia and Myelodysplastic Syndrome: A Meta-Analysis of Randomized Controlled Trials. Front Onc...
Introduction: HLH syndrome is a rare but life-threatening condition of severe hyperinflammation caused by uncontrolled proliferation of activated lymphocytes and macrophages secreting high amounts of inflammatory cytokines. It can present in adults as a Sepsis mimic. Case 71-year-old Caucasian male with...
THU0557鈥匟aemophagosytic Limphohistiosytosis (HLH) in Adults. Diseases Triggers, Course, Treatment and Pronostic Factors. Differences Between Patients with Macrophage Activation Syndrome (MAS) and Other Causes of Secundary Heamophagosytic Limphohistiosytosis (SHLH). report Of Thirty-Two Cases...
While CCS is easily recognized in that patients have acute COVID-19 infection, HLH can be challenging to differentiate from other inflammatory syndromes. One such syndrome is adult-onset Still’s disease (AOSD), which, like HLH, presents with fever and extreme hyperferritinemia. However, the ...
Larger studies enriched with patients who have T-cell activation such as lymphoma, leukemia, and autoimmune lymphoproliferative syndrome are needed to better define the specificity of increased sIL-2r for both adult and pediatric HLH. Two recent important developments in the diagnosis of HLH are ...
Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome characterized by excess immune activation leading to inflammatory cytokine overproduction and hemophagocytosis [1]. Such a phenomenon of hyperinflammation can be either familial or acquired in origin with the most common causes including...
This review aims to provide physicians with an overview of the potential of procalcitonin to guide antibiotic therapy in respiratory tract infections and i... M Carmo,P Arumugam,S Tiwari,... - 《Swiss Medical Weekly》 被引量: 254发表: 2009年 A Griscelli syndrome type 2 murine model of hem...
hypocomplementemia, low grade DIC, confirmed bilateral retinitis and nephritis consistent with HLH. The underlying autoimmune dysfunction was thought to be secondary to XLP 2 as X-linked lymphoproliferative (XLP 1) and autoimmune lymphoproliferative syndrome(ALPS) were subsequently ruled…show more content...
Hemophagocytic syndrome in elderly patients with underlying autoimmune diseases. Clin Rheumatol. 2009;28:461–4. 5. Erdős M, Uzvölgyi E, Nemes Z, et al. Characterization of a disease-causing mutation of SH2D1A in a family with X-linked lymphoproliferative disease. Hum Mutat. 2005;25:...
噬血性淋巴组织细胞增生症(hemophagocytic lymphohistiocytosis,HLH),又称噬血细胞综合征(hemophagocytic syndrome,HPS),是一组较为少见、由活化的淋巴细胞和组织细胞增生引起的多器官高炎症反应而又免疫无效的临床综合征,起病急、病情进展迅速、病死率高。主要特征为发热、肝脾肿大、血细胞减少和组织细胞噬血现象(主要见于...