childrenliver diseaseHemophagocytic lymphohistiocytosis (HLH) is a rare acute hyperinflammatory condition presenting with high fever, pancytopenia, splenomegaly with the pathologic finding of hemophagocytic lymphohistiocytosis in bone marrow and other tissues. Predominant hepatic manifestations at presentation are ...
Hemophagocytic lymphohistiocytosis(HLH)is a critical hematological disorder characterized by immune dysfunction with multiple organs and systems involved.HLH secondary to rheumatic disease is also named as macrophage activation syndrome(MAS). In children, MAS is often covered by primary diseases so that it...
We report a series of three cases which showcase the spectrum of liver disease as presentation in hemophagocytic lymphohistiocytosis.关键词: HLH children liver disease CMV, cytomegalovirus EBV, Epstein Barr virus HLH, hemophagocytic lymphohistiocytosis LKM, liver–kidney-microsomal MAS, macrophage ...
in ch il dr en w i th H L H -200 4 p r otocol Z H U Y in, GA0 Y i-j in,ZHU Xiao— hua,CHEN X iao— yun ( Children" s Hospital o f Fudan University ,Shanghai China) Abstract: Obj ective Hemophagocytic lymphohistiocytosis ( HLH) is a pediatr i c disease with ...
HLH consists of two forms: familial and acquired, the latter which occurs in association with infection, malignancy, rheumatic disease and acquired immune deficiency. Herein, we report a case of acquired HLH in a child who had received allogeneic hematopoietic stem cell transplantation for familial ...
具有不同树突状细胞表型的孤立性组织细胞瘤（solitaryhistiocytomasofvariousdendriticcellphenotypes）巨噬细胞相关性疾病（Macrophage-relateddisorders）原发性或继发性噬血细胞综合征（Hemophagocyticsyndrome，primaryorsecondary）罗-道病(Rosai-Dorfmandisease，RD)(淋巴结窦组织细胞增生症伴广泛淋巴结肿大，sinushistiocytosis...
关键词:噬血淋巴组织细胞增生症;儿童;系统评价;Meta分析 万方数据 ASSESSMENToFHLH.94ANDHLH.04 IMMUNoCHEMoTHERAPYPRoTOCoLFoR IN CHILDREN:ASYSTE^僵ATICREVIEWANDMETA ANALYSIS ABSTRACT ectiVe a rare obj Hemophagocytic diseasecharacte“zeduncontrolled onthebasis 伊aVe by hyperinn猢ation ofVa矗ous iIlllerited...
[Clinical characteristics and disease course in children with haemophagocytic lymphohistiocytosis treated at the University Children's Hospital in Belgrade]. Introduction. Haemophagocytic lymphohistiocytosis (HLH) is a disorder characterised by long-standing fever, splenomegaly and bicytopoenia or pancytopoe...
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Most patients are young children; signs and symptoms include changes in blood cell counts, enlarged liver and spleen, enlarged lymph nodes, and rash.Treatment is by chemotherapy and in some cases bone-marrow transplantation.Hemophagocytic lymphohistiocytosis is also known as HLH disease. See also ...