Results: All patients had the CREST variant of scleroderma. Their average age was 48.6 years (range 35-56). All had arthropathy affecting mainly the hands and feet. In the majority of cases the clinical picture resembled that of RA, with inflammation and subluxation of the metacarpophalangeal ...
sclerodermapulmonary hypertensionnifedipineA patient with severe pulmonary hypertension secondary to the CREST syndrome variant of scleroderma is described. Acute reductions in both pulmonary artery pressure and total pulmonary resistance were seen with nifedipine and oxygen administration. Reductions in ...
Follansbee WP, Curtiss EI, Medsger TA, et al.: Myocardial function and perfusion in the CREST syndrome variant of progressive systemic sclerosis: exercise radionuclide evaluation and comparison with diffuse scleroderma. Am J Med 77: 489–496, 1984. PubMed CAS Google Scholar Escalante A, Beardmore...
摘要: We report a case of bilateral associated with the , a variant of . Immunosuppressive therapy achieved significant improvement of the visual symptoms for two years. The pathophysiological mechanisms underlying this unique association remain unclear.关键词:...
(Table 55.3); scleroderma (hard skin) is the most specific and prominent physical finding. Patients vary in the expression of the skin changes and are classified into two major subsets defined by the degree of clinically involved skin. In the diffuse skin variant calleddiffuse cutaneous SSc(dcS...
Overlap syndromes are common in systemic sclerosis and can involve conditions such as rheumatoid arthritis and polymyositis. Additionally, patients with systemic sclerosis have an elevated risk of psychological disorders such as depression, affecting up to 50% of individuals. Another variant, systemic scle...
ACA was found almost exclusively (96%) in patients with limited cutaneous scleroderma (the CREST syndrome variant), but the majority (57%) of patients ... Virginia,D.,Steen,... - 《Arthritis & Rheumatism》 被引量: 1109发表: 1988年 Expression of osteonectin and matrix Gla protein in sclero...
Owens GR, Fino GJ, Herbert DL, Steen VD, Medsger TA Jr, Pennock BE, Cottrell JJ, Rodnan GP, Rogers RM (1983) Pulmonary function in progressive systemic sclerosis. Comparison of crest syndrome variant with diffuse scleroderma. Chest 84:546–550 ...
The CREST syndrome (calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, telangiectasia) is a variant but not a benign form of sclerode... J,T,Lie - 《Angiology》 被引量: 5发表: 1989年 Study on the clinical characteristics of systemic sclerosis BACKGROUND: Systemic sclerosis...
Pathologic observations in systemic sclerosis (scleroderma). A study of fifty-eight autopsy cases and fifty-eight matched controls. Pulmonary hypertension in the crest syndrome variant of systemic sclerosis Systemic sclerosis: a prototypic multisystem fibrotic disorder ...