Idiopathic pulmonary fibrosis (IPF) is a clinical syndrome of unknown cause affecting primarily middle aged or elderly patients. IPF follows an inexorably progressive and, usually, fatal course. It is associated with the histopathological pattern of usual interstitial pneumonia on surgical lung biopsy (...
Lung/ Pulmonary fibrosis is a chronic lung disease defined pathologically by abnormal and excessive deposition of extra-cellular matrix (ECM) and remodelling of pulmonary architecture. From: Pathology - Research and Practice, 2023 About this pageSet alert ...
Pediatric lung disease: from proteinases to pulmonary fibrosis. Pediatr Pulmonol 2005; 39: 392-401.Chua F, Sly PD, Laurent GJ. Pediatric lung disease: from proteinases to pulmonary fibrosis. Pediatr Pulmonol. 2005; 39 :392–401. doi: 10.1002/ppul.20171. [ Cross Ref ]...
People with a history of smoking were three times more likely to have pulmonary fibrosis or know someone affected by the disease, the findings showed."Awareness of pulmonary fibrosis and its symptoms remains very low, and for many, the first time they hear of it is when they are diagnosed,...
Pulmonary Fibrosis Drawing attention to a lung disease that is often overlooked. Being short of breath is the harsh reality for those living with pulmonary fibrosis, a relentless lung disease that scars and damages the lungs. Read more Pulmonary Fibrosis ...
Pulmonary Fibrosis Drawing attention to a lung disease that is often overlooked. Being short of breath is the harsh reality for those living with pulmonary fibrosis, a relentless lung disease that scars and damages the lungs. Read more Pulmonary Fibrosis ...
Learn about Esbriet® (pirfenidone), a medication for the treatment of idiopathic pulmonary fibrosis (IPF), a progressive and irreversible fibrotic interstitial lung disease. See full safety for more information.
Fibrosis, or scar tissue, develops and prevents the lungs from working normally. This gradually interferes with a person’s ability to breathe and function. IPF belongs to a family of more than 100 related diseases, called interstitial lung diseases (ILDs), which often have similar characteristics...
Pulmonary fibrosis results from dysregulated lung repair and involves multiple cell types. The role of endothelial cells (EC) in lung fibrosis is poorly understood. Using single cell RNA-sequencing we identified endothelial transcription factors involved
Idiopathic pulmonary fibrosis (IPF) is a progressive devastating lung disease with substantial morbidity. It is associated with cough, dyspnea and impaired quality of life. If left untreated, IPF has a median survival of 3 years. IPF affects ∼3 million people worldwide, with increasing incidence...