(1994) Peroxisomal acyl-coenzyme A oxidase is a rate-limiting enzyme in a very- long-chain fatty acid beta-oxidation system. Biochem. Biophys. Res. Commun., 201, 1541-1547.Aoyama T, Souri M, Kamijo T, Ushikubo S, Hashimoto T (1994a) Peroxisomal acyl-coenzyme A oxidase is a rate- ...
Human Peroxisomal acyl-coEnzyme A oxidase 1, ACox1 GENLISA™ ELISA Kit 供应商 Krishgen 产品货号 KBH4164 产品报价 ￥询价/1x96wells 产品说明书 点击查看 购买方式 90%产品中国有现货库存。银行转账、电汇、支票、现金,在线支付宝及网银支付,或直接与我们电话联系400-6800-868 产品新闻 背景资料 用于评估血...
Peroxisome targeting signal of rat liver acyl-coenzyme A oxidase resides at the carboxy terminus. To identify the topogenic signal of peroxisomal acyl-coenzyme A oxidase (AOX) of rat liver, we carried out in vitro import experiments with mutant polypept... S Miyazawa,T Osumi,T Hashimoto,......
neonatal adrenoleukodystrophy; IRD, infantile Refsum disease; AOXD, acyl-CoA oxidase 1 deficiency; DBPD, D-bifunctional protein deficiency; RCDP, rhizomelic chondrodysplasia punctata; X-ALD, X-linked adrenoleukodystrophy; RD, Refsum disease; AMACRD, 2-methylacyl-CoA racemase deficiency; N, normal;...
Fibrates downregulate apolipoprotein C-III expression independent of induction of peroxisomal acyl coenzyme A oxidase. A potential mechanism for the hypoli... Fibrates downregulate apolipoprotein C-III expression independent of induction of peroxisomal acyl coenzyme A oxidase. A potential mechanism for ...
Hepatocellular and hepatic peroxisomal alterations in mice with a disrupted peroxisomal fatty acyl-coenzyme A oxidase gene. MS, Maeda N, Reddy JK (1996) Hepatocellular and hepatic peroxisomal alterations in mice with a disrupted peroxisomal fatty acyl-coenzyme A oxidase gene. ... CY Fan,J Pan,R...
英文别名: ACOX2 (Acyl-Coenzyme A Oxidase 2, Branched Chain, BCOX, BRCACOX, BRCOX, THCCox, Peroxisomal Branched Chain Acyl-CoA Oxidase, THCA-CoA Oxidase, Trihydroxycoprostanoyl-CoA Oxidase) (AP) 中文名: 中文别名: CBNumber: CB04969749 分子式: 分子量: 0 MOL File: Mol file 化学...
The concentration of pristanic acid was measured in plasma from a patient with an isolated peroxisomal very long chain fatty acid (VLCFA) acyl-CoA oxidase deficiency, a defect in peroxisomal β -oxidation resulting in accumulation of VLCFA in plasma and tissues. Although peroxisomes are believed ...
Using complementation analysis, 24 were found to be deficient in enoylcoenzyme A hydratase/3-hydroxyacylcoenzyme A dehydrogenase bifunctional enzyme and 5 were deficient in acyl-CoA oxidase. Elevated plasma very long-chain fatty acids (VLCFA), impaired fibroblast VLCFA beta-oxidation, decreased ...
Clinical, biochemical, and mutational spectrum of peroxisomal acyl-coenzyme A oxidase deficiency. Peroxisomal acyl-coenzyme A (acyl-CoA) oxidase deficiency is an autosomal recessive inborn error of peroxisomal fatty acid oxidation due to a deficiency of... S Ferdinandusse,S Denis,EM Hogenhout,......