憩室黏膜正常,无分泌物、血潴留。结合临床影像学表现,诊断为Mounier-Kuhn综合征(Mounier-Kuhn syndrome,MKS),又称巨气管支气管症。 图1 HRCT(轴位面)示气管扩张(D1 - D2水平横径32.1 mm),右侧气管后外侧憩室(A,黑色箭头),多平面重建矢状面和冠状面(B,...
讨论：气管支气管巨大症(Mounier-Kuhn syndrome, MKS)又称(Tracheo broncho megaly,TBM)，是一种以气管、支气管管径明显增大可合并气管憩室、支气管扩张及下呼吸道反复感染为主要症状的罕见疾病。发病率约为1%~ 4.5%[1],Krustins等⑵报道其在有肺部症状的患者中发病率约为0.4%~1.6%。胸部X线摄影可显示气管、...
Background and aim: Mounier-Kuhn syndrome (MKS) is a congenital disorder characterized by tracheobronchomegaly resulting from the absence of elastic fibers in the trachea and main bronchi or atrophy and thinning of the smooth muscle layer. In this syndrome, dead space associated with tracheobroncho...
根据影像学表现,诊断为莫-昆综合征(Mounier-Kuhn syndrome, MKS)。未给予任何治疗,建议随访。 展开阅读 图1 患者女,23岁,4型Mounier-Kuhn综合征 1A 胸部侧位X线片示气管前后径增宽,气管前壁呈波浪状改变(箭) 1B 胸部CT平扫肺窗示隆突上2 cm处气管横径为3.9 cm 1C 胸部CT平扫肺窗示左、右支气管横径...
Mounier-Kuhn综合征(Mounier-Kuhn syndrome, MKS)又称气管支气管巨大症,是一种罕见的气道疾病,好发于男性 [ 1 ],以气管、主支气管及远端支气管扩张为特征,由Mounier-Kuhn于1932年首次对其描述而得名 [ 2 ]。该病目前病因不明,临床特征非特异。KMS患者呼气期间,气道塌陷,可引起呼吸道分泌物滞留,并反复发生呼吸...
The latter is termed Mounier- Kuhn syndrome (MKS) a condition which is characterized by pathologic dilatation of the tracheobronchial tree associated with elastic fiber and smooth muscle atrophy, along with respiratory infections [[4], [5], [6]]. In the current classification system, there are...
目的 分析3例巨气管支气管症(tracheobronchomegaly,TBM),即莫-昆综合征(Mounier-Kuhn syndrome)患者的临床特征,以提高对该病的认识,从而有利于早期诊断和治疗并发症,... 孙兵,代华平 - 《中华结核和呼吸杂志》 被引量: 5发表: 2011年 以体位相关性咳喘为主要症状的女性Mounier-Kuhn综合征一例并文献复习 Mounier...
Mounier-Kuhn syndrome or tracheobronchomegaly is a rare congenital condition, the management of which is complex. We report the case of a patient who was treated with interventional endoscopy. We describe the case of a 74-year-old man with a diagnosis of tracheobronchomegaly who was admitted ...
Mounier-Kuhn syndrome (MKS) should be considered as a rare cause of bronchiectasis, also in Africa. The presence of dilated trachea and bronchi with diverticula on chest-CT should make one highly suspicious of the diagnosis. Management is usually supportive with avoidance of air pollutants, vaccina...
Mounier-Kuhn syndrome is a rare idiopathic clinical, radiological and bronchoscopic disorder characterised by abnormal dilatation of the tracheo-bronchial tree. The usual presentation is with recurrent lower respiratory tract infections. Herein, we report the case of an adult male who was diagnosed to ...