参考文献: [1]. Saad MA, Ahmed H, Elgohary R, El Gendy HI: IgG4 related pericardium and lung disease in pediatric patient complicated with fatal massive hemoptysis: a case report and review of literature. Pediatric Rheumatology 2023, 21(1). [2]. Kamisawa T, Zen Y, Pillai S, Stone JH...
4(44%) patients had bilateral orbital involvement, while the remaining 5(55%) had unilateral disease. Conclusion: Ophthalmic involvement is a feature of IgG4-RD and has significant implications regarding the diagnosis, prognosis, and treatment of patients with IgG4 disease....
IgG4-related disease. IgG4-related disease (IgG4-RD) is considered a fibro-inflammatory condition with a marked propensity to form mass forming lesions, characterized by a dense... K Hirabayashi,G Zamboni - 《Pathologica》 被引量: 19发表: 2012年 The Geoepidemiology and Clinical Aspects of ...
A. et al. Functional analysis of the anti-adalimumab response using patient-derived monoclonal antibodies. J. Biol. Chem. 289, 34482–34488 (2014). Article PubMed PubMed Central Google Scholar Kamisawa, T. et al. A new clinicopathological entity of IgG4-related autoimmune disease. J. ...
IgG4-related disease characterized by an elevation of serum IgG4 (sIgG4) and infiltration of IgG4-positive plasma cells in the bile duct, as well as an overproduction of T-helper2 cells.1 The extrahepatic bile duct is often involved and also ...
However, the patient’s disease course was chronic relapsing during the first years. In the last 8 years before referral, however, the disease changed to a more chronic, stable course without major complications. When we saw the patient first in 2012, her medication included azathioprine 100 mg...
IgG4-related disease (IgG4-RD) was recently described in Japan. It is characterised by extensive organ involvement with tissue fibrosis. We assessed the performance of the 2019 American College of Rheumatology and European League Against Rheumatism (ACR/
Concomitant serological elevation of IgG4 levels may develop5,6; it was not evaluated in our patient but should probably be sought in orbital pseudotumors. Other IgG4-related diseases include autoimmune pancreatitis, sclerosing orbital inflammatory disease, Riedel struma, and retroperitoneal fibrosis.7 ...
We report a patient of 32-year-old female with central IgG4-related disease. She developed headache and visual disturbance. On examination, she revealed diabetes insipidus, retrobulbar neuritis, hyperreflexia and limb weakness. Her laboratory findings showed serum IgG4 elevation, pleocytosis and prote...
We retrospectively collected patient information such age at diagnosis, number of organs ever involved, IgG4 serum levels at diagnosis and/or during the disease course, biopsy availability and the use of glucocorticoids and immunosuppressive therapy. Patients were classified according to clinical phenotypes...