Our recent studies have shown that the amyloid fibril protein in Finnish hereditary amyloidosis (familial amyloid polyneuropathy type IV) is a new type of amyloid protein that is a fragment of variant gelsolin, a cytoskeletal and plasma protein with actin-modulating properties. Antibodies against a ...
Gelsolin (Amyloidosis, Finnish Type) Antibody is a Rabbit Polyclonal antibody against Gelsolin (Amyloidosis, Finnish Type).
Our study shows that deposition of AGel in the spinal and cerebral blood vessel walls, meninges, as well as spinal nerve roots and sensory ganglia is an essential feature of this form of systemic amyloidosis and may contribute to the central nervous system symptoms.Ann Neurol 1999;45:305–311...
Hereditary gelsolin amyloidosis (HGA) is an autosomally dominantly inherited form of systemic amyloidosis, characterized mainly by cranial and sensory peripheral neuropathy, corneal lattice dystrophy, and cutis laxa. HGA, originally reported from Finland and now increasingly from other countries in Europe...
免疫原 gelsolin(amyloidosis, Finnish type) 分子量 87-93 kDa Uniprot ID P06396 适用种属 Human, Mouse, Rat 验证应用 ELISA, WB, IHC 建议稀释比例 WB: 1:500-1:2000; IHC: 1:20-1:200 图片 Immunohistochemistry of paraffin-embedded human colon cancer using FNab03417(GSN antibody) at dilution ...
英文名称:Gelsolin (Amyloidosis, Finnish Type) Antibody 北京启维益成科技有限公司 联系电话:010-82743161 电子邮件:info@qwbio.com CB指数:50 网址:www.qwbio.com 相关信息:产品目录(6912)用户评价 英文名称:Gelsolin (Amyloidosis, Finnish Type) Antibody ...
Familial amyloidosis, Finnish type (FAF), is an inherited form of systemic amyloidosis clinically characterized by cranial neuropathy and lattice corneal dystrophy. We have demonstrated that the protein subunit isolated from amyloid fibrils shows considerable sequence identity with gelsolin, an actin-binding...
www.nature.com/scientificreports OPEN Molecular basis of a novel renal amyloidosis due to N184K gelsolin variant received: 28 June 2016 accepted: 16 August 2016 Published: 16 September 2016 Francesco Bonì1,2, Mario Milani1,2, Riccardo Porcari3, Alberto Barbiroli4, Stefano Ricagno2 ...
Full Name gelsolin (amyloidosis, Finnish type) Synonyms Actin depolymerizing factor, ADF, AGEL, Brevin, Gelsolin, GSN Calculated Molecular Weight 782 aa, 86 kDa Observed Molecular Weight 80-83 kDa GenBank Accession Number BC026033 Gene Symbol Gelsolin Gene ID (NCBI) 2934 RRID AB_2881663 Conjug...
英文别名Actin-depolymerizing factor | ADF | AGEL | Brevin | DKFZp313L0718 | gelsolin (amyloidosis, Finnish type) | Gelsolin | GSN | Actin depolymerizing factor antibody | Actin-depolymerizing factor antibody | ADF antibody | AGEL antibody | Brevin antibody | DKFZ ...