1.von Samson-Himmelstjerna FA, Kakavand N, Voran JC, et al. Use of Immunoadsorption and Plasma Exchange for Treating Anti-Glomerular Basement Membrane Disease: Clinical Experience in Germany. Am J Kidney Dis. 2024 Feb 29:S02...
1. National Kidney Foundation.National Kidney Foundation 2022 Spring Clinical MeetingAbstracts. ANTIBODY NEGATIVE ANTI-GBM DISEASE PRESENTING AS GROSS HEMATURIA INAN 82-YEAROLD PATIENT. AJKD. 2022 April. 2.AsimM, Akhtar M. Epi...
一、简介 抗肾小球基底膜病(Anti-GBM disease)是一种罕见但危重的自身免疫性疾病,属于小血管炎,其特点是体内产生针对肾小球基底膜(GBM)和肺泡基底膜(ABM)的自身抗体。这些抗体可导致: 快速进展性肾小球肾炎(RPGN):急性肾功能下降,伴血尿和蛋白尿。 肺泡出血(Alveolar hemorrhage):咯血、呼吸困难及影像学异常。 ...
[3]2019年美国血浆置换学会血浆置换学会血浆置换和免疫吸附临床实践指南(第8版)解读.中华肾病研究电子杂志,2021,10(1):8-13. [4]AsimM,Akhtar M,Epidemiology,impact,and management Strategies of Anti-GlomerularBasement Membrane Disease.Int J Nephrol Renovasc Dis.2022 Apr7;15:129-138. [5]系统性血管炎...
whichcontainstheepitopesE.andEr.Thehumoralandcellularimmunitycontributingtotheinitiationofanti-GBMdiseasehasbeenextensivelystudiedasamodelforautaimmtmostofthedayInthisRevewwesummarizethecurrentknowledgeontheprevalence,clinicalmanifestations,treatmentandoutcomesofhumanantGBMdiseaseWediscussfindingsonpathogenesiiseInitonand...
抗肾小球基底膜(GBM)病 热度: 抗GBM病的进展 抗GBM病的背景 抗GBM病是以循环中出现抗GBM抗体及其在脏器中沉积为特征的自身免疫性疾病 1919:Goodpasture首先报道 1例18岁男性病人,咯血、急性肾衰竭 1967:Lerner等发现抗GBM抗体 1988:Saus等发现3(IV)NC1为主要靶抗原 ...
抗肾小球基底膜(GBM)病 抗肾小球基底膜(GBM)病 抗GBM病的背景 •抗GBM病:循环中出现抗GBM抗体、脏器中沉积为特征的自身免疫病 •1919:Goodpasture首先报道 –1例18岁男性病人,咯血、急性肾衰竭–主要累及肺和肾脏:Goodpasture病 •内科危重症:危及生命•80%就诊时已进入尿毒症(ESRD)GoodpasureEM.AmJ...
697-706GBM4HudsonGB.VanderbiltUniversityGBMmoleculararchitectureofconformationalepitopesPuseyCD.HammersmithImperialCollegeLondonPEinanti-GBMdiseaseWKYratmodelGeneticsofEAGmodelsSegelmarkM&WieslanderJLundUniversityRecombinantantigensDetectionofanti-GBMdiseaseZhaoMH&CuiZPekingUniversityHumananti-GBMdiseaseLinearepitopes...
抗GBM病的进展 抗GBM病的进展 1 抗GBM病的背景 抗GBM病是以循环中出现抗GBM抗体及其在脏器中沉积为特征的自身免疫性疾病1919:Goodpasture首先报道 1例18岁男性病人,咯血、急性肾衰竭 1967:Lerner等发现抗GBM抗体 1988:Saus等发现3(IV)NC1为主要靶抗原 GoodpasureEM.AmJMedSci1919;...
López-González Gila JD, Aguilar Jaldo MP, Plata Sánchez RM, Mañero Rodríguez CA. Anti-GBM disease associated with extracorporeal shock wave lithotripsy (ESWL). Int Urol Nephrol. 2023 Jun 6. doi: 10.1007/s11255-023-03657-3. Epub ahead of print. PMID: 37280315. ...