细胞肉毒碱棕榈酰转移酶II(CARNITINE PALMITOYL-TRANSFERASE II)活性比色法定量检测试剂盒 价格电议 起批量≥1 盒 最小起订1盒 供货总量90盒 发货地址广东省深圳市 建议售价￥1/盒 更新日期2025年02月13日 即时洽谈立即询价查看联系方式 收藏产品发送留言 ...
Carnitine palmitoyltrans- ferase 2: New insights on the substrate specificity and implications for acylcarnitine profiling. Biochim Biophys Acta. 2010; 1802: 728-732. doi: 10.1016/j.bbadis.2010.06.002 PMID: 20538056Violante S, et al. Carnitine palmitoyltransferase 2: new insights on the substrate...
Carnitine Palmitoyl Transferase-2 (CPT-2) 供应商 MyBioSource 产品货号 MBS614466 产品报价 ￥询价/0.1mL ￥询价/5x0.1mL ￥询价/其它规格 产品说明书 点击查看 购买方式 MyBioSource中国区金牌代理,部分产品现货库存。银行转账、电汇、支票、现金,在线支付宝及网银支付,或直接与我们电话联系400-6800-868 ...
Carnitine Palmitoyl Transferase 2 (CPT-2) 供应商 MyBioSource 产品货号 MBS612629 产品报价 ￥询价/0.1mg ￥询价/5x0.1mg ￥询价/其它规格 产品说明书 点击查看 购买方式 MyBioSource中国区金牌代理,部分产品现货库存。银行转账、电汇、支票、现金,在线支付宝及网银支付,或直接与我们电话联系400-6800-868 ...
Carnitine Palmitoyl Transferase 2 Deficiency Themitochondrial oxidationof fatty acids is the main source of energy for muscles during prolonged exercise and during fasting. Thecarnitinepalmitoyl transferase (CPT)enzymesystem is essential for the transfer of fatty acids across themitochondrial membrane....
Article: Carnitine palmitoyl transferase ii deficiency with normal carnitine palmitoyl transferase i in skeletal muscle and leukocytes
JW-S51036组织肉毒碱棕榈酰转移酶II(CARNITINE PALMITOYL-TRANSFERASE II)活性比色法定量检测试剂盒 JW-S53766营养添加剂肉毒碱(carnitine,左卡尼丁)含量比色法(412)定量检测试剂盒 JW-S52419植物非蛋白/游离巯基含量荧光定量检测试剂盒 JW-S51072组织长链脂酰辅酶A氧化酶(acyl-CoA oxidase)活性比色法定量检测试剂盒...
Neonatal Carnitine Palmitoyl Transferase Deficiency Type II, characterized by the absence of CPT II enzyme, is one of the lethal disorders of mitochondrial fatty acid oxidation. CPT II regulates the conversion of long chain fatty acids, so that its product, acyl-CoA esters, can enter the Krebs ...
Carnitine palmitoyl transferase II (CPT II) deficiency is a lipidosis and is a common cause of inherited recurrent myoglobinuria. The disease is inherited in autosomal recessive trait, and the clinical phenotype ranges from a severe and multisystemic infantile form to a milder muscle form, which ...
1.an enzyme that reversibly forms acylcarnitines and coenzyme A from carnitine and acylcoenzyme A (often, palmitoyl-CoA); important in fatty acid oxidation. Deficiency of isozyme I results in ketogenesis with hypoglycemia; deficiency of isozyme II affects primarily skeletal muscle. ...