Carnitine palmitoyltransferase 2 (CPT2Long-chain acyl-CoAFatty acid oxidation (FAOMitochondrial Trifunctional Protein (MTPOver the last years acylcarnitines have emerged as important biomarkers for the diagnosis of mitochondrial fatty acid β-oxidation (mFAO) and branched-chain amino acid oxidation ...
肉碱棕榈酰基转移酶II缺乏症的英文名字是Carnitine Palmitoyltransferase II Deficiency。基因解码表明:佳学基因通过基因解码发现:肉碱棕榈酰基转移酶II缺乏症是由基因突变引起的。这种疾病是由于基因CPT2的突变导致肉碱棕榈酰基转移酶II的功能缺陷,从而影响脂肪酸的氧化代谢。这种基因突变可以是遗传的,也可以是新生突变。
Figure 27.1.Carnitine cycle pathway involving carnitine palmitoyltransferase 2. CACT, carnitine:acylcarnitine translocase;CPT1, carnitine palmitoyltransferase 1;CPT2, carnitine palmitoyltransferase 2;FATP, fatty acid transport proteins;MTFP, mitochondrial trifunctional protein. ...
CPT2 carnitine palmitoyltransferase 2 CPT2 antibody CPT2 gene knockdown CPT2 cDNA CPT2 protein CPT2 other total:1 Coimmunoprecipitation of FAT/CD36 and CPT I in skeletal muscle increases proportionally with fat oxidation after endurance exercise training. 2006to the paper ...
Section > Chapter Scholte, H.R.; Jennekens, F.G.I.; Bouvy, J.J.B.J. Journal of the Neurological Sciences 40(1): 39-52 1979 ISSN/ISBN:0022-510X 004884312 Full-Text Article emailed within 1 workday Buy Now for$29.90 Payments are secure & encrypted ...
中文名称:CPT2 (Carnitine O-palmitoyltransferase 2, Mitochondrial, Carnitine Palmitoyltransferase II, CPT1, IIAE4, CPTASE) (AP) 中文同义词: 英文名称:CPT2 (Carnitine O-palmitoyltransferase 2, Mitochondrial, Carnitine Palmitoyltransferase II, CPT1, IIAE4, CPTASE) (AP) ...
We used lentiviral shRNA to knock down the expression of medium-chain acyl-CoA dehydrogenase (MCAD) in control and carnitine palmitoyltransferase 2 (CPT2)-, carnitine/acylcarnitine translocase (CACT)-, and plasmalemmal carnitine transporter (OCTN2)-deficient human fibroblasts. These cell lines, ...
Carnitine O-palmitoyltransferase 2, mitochondrial Kind protein Organism Humans Protein NameUniProt ID Carnitine O-palmitoyltransferase 2, mitochondrial P23786 Details Drug Relations Drug Relations Show entries DrugBank IDNameDrug groupPharmacological action?ActionsDetails DB00583 Levocarnitine approved, investigati...
CPT2 (Carnitine O-palmitoyltransferase 2, Mitochondrial, Carnitine Palmitoyltransferase II, CPT II, CPT1) 供应商 MyBioSource 产品货号 MBS649254 产品报价 ¥询价/0.1mg ¥询价/5x0.1mg ¥询价/其它规格 产品说明书 点击查看 购买方式 MyBioSource中国区金牌代理,部分产品现货库存。银行转账、电汇、支票、现金...
The exonic regions of the carnitine palmitoyltransferase 2 ( CPT2) gene were characterized from 101 patients with defined clinical and biochemical evidence... PJ Isackson,MJ Bennett,GD Vladutiu - 《Molecular Genetics & Metabolism》 被引量: 69发表: 2006年 Two novel gene mutations (Glu174→Lys, ...