Suspected cardiac amyloidosis: endomyocardial biopsy remains the diagnostic gold-standard. Am J Hematol. 2007;82(4):328.Kristen AV, Dengler TJ, Katus HA (2007) Suspected cardiac amyloidosis: endomyocardial biopsy remains the diagnostic gold-standard. Am J Hematol 82:328...
However, endomyocardial biopsy is the definitive diagnostic, recent developments in imaging techniques and extracardiac tissue sampling have minimized the need for invasive endomyocardial biopsy for amyloidosis. Despite advances in treatment, the prognosis for patients with amyloidosis is still poor and ...
Abstract 16230: Genetically Confirmed Hypertrophic Cardiomyopathy, Initially Misdiagnosed as Cardiac Amyloidosis by Cardiac Biopsydoi:10.1161/circ.148.suppl_1.16230... YR Kim,HS Sang,YS Chang,... - 《Circulation》 被引量: 0发表: 2023年 Left atrial reservoir strain differentiates cardiac amyloidosis an...
[Value of cardiac magnetic resonance imaging for the diagnosis of cardiac amyloidosis]. To observe the clinical features and cardiac magnetic resonance imaging (CMR) characteristics of patients with endomyocardial biopsy (EMB)-proven cardiac a... KB Zhu,ZW Cheng,T Zhuang,... - 《Zhonghua Xin Xue...
The gold standard diagnostic test is right-ventricular biopsy, which demonstrates positivity for Congo Red staining. Due to a propensity for disease progression, typically low systemic blood pressure, frequent extra-cardiac involvement and autonomic dysfunction, cardiac amyloidosis is difficult to treat ...
The diagnosis of cardiac amyloidosis is very hard and can easily be misdiagnosed. Although the imaging studies (such as echocardiography and cardiovascular magnetic resonance) may guide the diagnosis, tissue biopsy is needed for confirmation. Management of cardiac amyloidosis initially is to treat the ...
9 A cardiac biopsy is often needed in such patients to obtain a definitive diagnosis.8 Hereditary transthyretin amyloidosis The transthyretin (TTR) gene is located on chromosome 18 and contains four exons and five introns. There are more than 120 mutations in the TTR gene, most of which encode...
A combination of hypertrophic obstructive cardiomyopahhy (HOCM) and cardiac amyloidosis in the same patient is very rare. Clinical diagnosis could be extremely difficult and may require myocardial biopsy. We are reporting a patient with this combination who was referred to our institution because of...
Endomyocardial biopsy: Biopsy is the gold-standard test for diagnosing cardiac amyloidosis. The biopsy shows characteristic salmon-colored amyloid fibrils on the ‘Congo-red’ stain. On electron microscopy, there is a characteristic ‘apple-green’ birefringence on polarized light. A cardiac biopsy is...
Cardiovascular magnetic resonance in clinically suspected cardiac amyloidosis: noninvasive imaging compared to endomyocardial biopsy. We sought to evaluate the diagnostic performance of cardiovascular magnetic resonance imaging (CMRI) for detection of cardiac amyloidosis compared with end... H Vogelsberg,H ...