Alpha-1-antitrypsineAlpha-1-antitrypsinedoi:[90-10-0100] -Doi : 10.1016/S0000-0000(09)48236-6Alpha-1-antitrypsin deficiency is the most common inborn error of metabolism leading to liver transplantation, and the second cause of liver transplantation in children after biliary atresia. The authors...
The existence of a seric deficiency in alpha-1-antitrypsin in certain chronic bronchopneumopathies now constitutes a definite clinical entity. The familial or individual nature of this deficiency is revealed by the early onset of a respiratory insufficiency. The case which we describe involves a 34...
Genetic variants were observed in this pattern either in alpha-1-antitrypsin deficient patients or normal subjects (Fagerhol). Among 100 apparently healthy blood donors, the authors were able to detect one subject Pi SS ; among 351 patients with lung disease of various types, they observed ...
By systematically exploring the ratio of active carbon,alumina and boron oxide,the best formulation and the corresponding reaction mechanism were determined.F. BonnometY. LefèbvreP. ClavertP. GicquelP. MarcillouM. KatznerJ.F. Kempf中国耐火材料(英文版)...
Alpha-1-antitrypsin deficiency is the most common inborn error of metabolism leading to liver transplantation, and the second cause of liver transplantation in children after biliary atresia. The authors report the case of a 6-year-old girl, who was suffering from end-stage liver disease secondary...
Serpin A1e/Alpha-1-antitrypsin 1-5Mouse 发布时间:2025/3/5 11:47:29 关注度:502 种 属:Human/Mouse/Rat 标 签:详询 规 格:10ug/50ug/500ug/1mg 缓 冲 液:0.01mol/L的PBS、pH:7.2、0.2%Procline-300。 表达宿主:E.coli/Cells 内毒素:经LAL检测验证,小于0.1ng/ul(0.1EU/ug) 纯化方法:亲和...
Validation d’une méthode de mesure de l’activité antiélastasique de l’alpha1-antitrypsine circulante humaineVolume 82, numéro 3, Mai-Juin 2024 PDF Imprimer Ajouter à mes favoris Citer cet article Envoyer un lien vers article Partag...
英文: Isolation and Purification of α1-Antitrypsin中文: α1-抗胰蛋白酶的分离纯化 英文: Advance in Fractionation and Application for Human α1-antitrypsin中文: α1-抗胰蛋白酶的分离纯化及应用研究进展 英文: Alpha 1-antitrypsin Matrix Attachment Region Enhances RNA PolymeraseⅡ-dependent Transcription...
Alpha1-antitrypsin (α1AT) is an abundant serine-protease inhibitor in circulation. It has an important role in neutralizing the neutrophil elastase activity. Different pathogenic point mutations like Z(E342K)-α1AT have been implicated in the devel
中文: α1-抗胰蛋白酶的研究进展 英文: Isolation and Purification of α1-Antitrypsin中文: α1-抗胰蛋白酶的分离纯化 英文: Advance in Fractionation and Application for Human α1-antitrypsin中文: α1-抗胰蛋白酶的分离纯化及应用研究进展 英文: Alpha 1-antitrypsin Matrix Attachment Region Enhances RNA ...