Your doctor will do a genetic test if they think you have a type that is passed down through families. Treatment for hereditary amyloidosis differs from that for other types of the disease. Once you’re diagnosed, your doctor might check your heart with anechocardiogramor your liver and spleen...
PROGNOSISAORTIC stenosisGrowing interest has accrued in the co-existence of cardiac amyloidosis and valvular heart disease. Amyloid infiltration from either transthyretin (ATTR) or of light chain (AL) origin may affect any structure of the heart, including the valves. The recent literature has mainly...
Survival in AL amyloidosis depends on the spectrum of organ involvement (amyloid heart disease being the main prognosis factor), the severity of individual organs involved and haematological response to treatment.Definition Amyloidosis belongs to the group of protein conformational diseases and results from...
Valvular heart disease in patients with cardiac amyloidosis 2024, Heart Failure Reviews Cardiac amyloidosis and aortic stenosis: a state-of-the-art review 2023, European Heart Journal Open Red Flags, Prognostic Impact, and Management of Patients With Cardiac Amyloidosis and Aortic Valve Stenosis: A ...
Prognosis is affected by the rate of synthesis and the concentration of the circulating precursor. Accurate diagnosis of the underlying disease is mandatory as the treatment is based on disease control and inhibition of amyloid precursor production. Organ-specific treatment, such as transplantation, ...
Summary Symptoms Duration Call doctor Prognosis More info What is amyloidosis?Amyloidosis is a disease in which an abnormal protein called amyloid accumulates in body tissues and organs. The protein deposits can be in a single organ or dispersed throughout the body. The disease causes serious ...
heart failure, Val30Met mutation results in lower extremity sensorimotor peripheral neuropathy. These patients typically present in 4th–6th decades of their life (Bejar et al., 2015; Galant et al., 2017). Orthotopic liver transplant can halt the disease in ATTR amyloidosis patients and can be ...
Amyloidosis is often classified into subtypes based on the body areas it affects, and symptoms are specific to those areas. The disease is often overlooked in its earliest stages because it does not cause symptoms. When there are symptoms, they are often mistaken for those caused by other condi...
Prognosis is affected by the rate of synthesis and the concentration of the circulating precursor. Accurate diagnosis of the underlying disease is mandatory as the treatment is based on disease control and inhibition of amyloid precursor production. Organ-specific treatment, such as transplantation, ...
Prognosis of patients with primary systemic amyloidosis who present with dominant neuropathy. CONCLUSIONS: Patients with primary systemic amyloidosis in whom neuropathy is the dominant clinical manifestation often do not receive a diagnosis until ye... RA Kyle - 《American Journal of Medicine》 被引量...