Bok LA, Struys E, Willemsen MA, Been JV, Jakobs C (2006) Pyridoxine dependent seizures in Dutch patients: diagnosis by elevated urinary alpha-aminoadipic semialdehyde dehydrogenase levels. Arch Dis Child Nov 6; [Epub ahead of print].Bok LA, Struys EA, Willemsen MA et al (2007) Pyridoxine-...
alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid Alpha-Aminoisobutyric Acid alpha-aminosuccinic acid Alpha-Amylase ▼ Complete English Grammar Rules is now available in paperback and eBook formats. Make it yours today! Advertisement. Bad banner? Pleaselet us knowRemove Ads...
This metabolite is derived from α-ketoadipic acid through the enzymatic conversion of α-aminoadipic semialdehyde by α-aminoadipic semialdehyde dehydrogenase. This α-AAA can serve as a precursor for the saccharopine pathway, which branches off the lysine pathway. Saccharopine is produced when α-...
alpha-amino-beta-ketoadipic acid Alpha-Amino-N-Butyric Acid Alpha-aminoadipate Alpha-aminoadipic acid Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid Alpha-Aminoisobutyric Acid alpha-aminosuccinic acid ▼Complete...
alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid Alpha-Aminoisobutyric Acid alpha-aminosuccinic acid alpha-amylase Alpha-Amylase Inhibitor from Lablab Purpureus alpha-antitrypsin alpha-beta brass alpha-beta brass alpha-beta brass Alpha-Beta Counting System Alpha-Beta Technology Inc. alp...
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Purification and characterization of a dehydrogenase catalyzing conversion of N alpha-benzyloxycarbonyl-L-aminoadipic-delta-semialdehyde to N alpha-benzylo... The enzyme catalyzing conversion of N α-benzyloxycarbonyl- L-aminoadipic-δ-semialdehyde ( N α-Z- L-AASA) to N α-benzyloxycarbonyl- L-amino...
Bok LA, Struys E, Willemsen MAAP, Been JV, Jakobs C (2007) Pyridoxine-dependent seizures in Dutch patients: diagnosis by elevated urinary alpha-aminoadipic semialdehyde levels. Arch Dis Child 92:687-689Bok LA, Struys E, Willemsen MA, Been JV, Jakobs C (2007) Pyridoxine-dependent seizures in...
Recently α-aminoadipic semialdehyde (α-AASA) dehydrogenase deficiency was identified as a major cause of PDS, which causes accumulation of both α-AASA and pipecolic acid (PA) in body fluids. Methods: We studied urinary and plasma α-AASA and PA levels in 12 Dutch clinically diagnosed ...
Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid Alpha-Aminoisobutyric Acid alpha-aminosuccinic acid Alpha-Amylase Alpha-Amylase Alpha-Amylase Alpha-Amylase Alpha-Amylase Inhibitor from Lablab Purpureus alpha-antitrypsin alpha-beta brass alpha-beta brass alpha-beta...