Recently described biochemical and molecular pathology improved the diagnostic process for those cases in which seizures are caused by alpha amino adipic semialdehyde dehydrogenase deficiency. This article presents a girl with recurrent status epilepticus episodes resistant to phenobarbital and phenytoin and ...
alpha-amino-3-hydroxy-5-methyl-4-isoxazolepropionate receptor alpha-amino-beta-ketoadipic acid Alpha-Amino-N-Butyric Acid Alpha-aminoadipate Alpha-aminoadipic acid Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid ...
Alpha-Amino-3-Hydroxy-5-Methyl-4-Isoxazole Propionic Acid alpha-amino-3-hydroxy-5-methyl-4-isoxazolepropionate receptor alpha-amino-beta-ketoadipic acid Alpha-Amino-N-Butyric Acid Alpha-aminoadipate Alpha-aminoadipic acid Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobuty...
This metabolite is derived from α-ketoadipic acid through the enzymatic conversion of α-aminoadipic semialdehyde by α-aminoadipic semialdehyde dehydrogenase. This α-AAA can serve as a precursor for the saccharopine pathway, which branches off the lysine pathway. Saccharopine is produced when α-...
alpha-amino acid Alpha-Amino-3-Hydroxy-5-Methyl-4-Isoxazole Propionic Acid alpha-amino-3-hydroxy-5-methyl-4-isoxazolepropionate receptor alpha-amino-beta-ketoadipic acid Alpha-Amino-N-Butyric Acid Alpha-aminoadipate Alpha-aminoadipic acid Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase...
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The corresponding amino acid residues in Mtb-DapA are Lys171, Arg148, Tyr117, Tyr143 and Thr54. Transposon mutagenesis experiments in M. tuberculosis showed that the genes of the DAP pathway, namely, aspartokinase (ask), aspartate-semialdehyde dehydrogenase (asd), dihydrodipicolinate synthase (...
The predominant product with most aldehydes is the L-erythro diastereomer. For example, succinic semialdehyde methyl ester is condensed with glycine in the process to provide L-erythro alpha -amino- beta -hydroxy adipic acid mono methyl ester.MILLER, MARVIN JOSEPH, SOUTH BEND, INDIANA , US...
The predominant product with most aldehydes is the L-erythro diastereomer. For example, succinic semialdehyde methyl ester is condensed with glycine in the process to provide L-erythro alpha -amino- beta -hydroxy adipic acid mono methyl ester.MILLER MARVIN JOSEPH...
alpha-amino-3-hydroxy-5-methyl-4-isoxazolepropionate receptor alpha-amino-beta-ketoadipic acid Alpha-Amino-N-Butyric Acid Alpha-aminoadipate Alpha-aminoadipic acid Alpha-aminoadipic acid alpha-aminoadipic semialdehyde dehydrogenase Alpha-Aminoisobutyric Acid Alpha-Aminoisobutyric Acid alpha-aminosuccinic acid...