6.Palladini G, Dispenzieri A, Gertz MA, et al. New criteria for response to treatment in immunoglobulin light chain amyloidosis based on free light chain measurement and cardiac biomarkers: impact on survival outcomes [J]. J Clin Oncol, 2012, 30 (36): 4541-4549. 7.Gustine JN, Staron A...
7. Lilleness B, Doros G, Ruberg FL, Sanchorawala V. Establishment of brain natriuretic peptide - based criteria for evaluating cardiac response to treatment in light chain (AL) amyloidosis. Br J Haematol. 2020;188(3):424-427. 8. Cornell R...
Figure 7.AL amyloidosis with randomlyarranged nonbranching fibrils with a diameter of 10-12 nm (electronmicroscopy). Reproduced with permission from AJKD 32(5):e1. - Am J Kidney Dis.2015;66(6):e43-e45 e45 Atlas of Renal Pathology II...
The most frequent presenting symptoms are asthenia and dyspnoea, which are poorly specific and may account for delayed diagnosis. Organ involvement in systemic AL amyloidosis is now defined by consensus criteria, which have been updated at the 2010 meeting of the International Society of Amyloidosis ...
The most frequent presenting symptoms are asthenia and dyspnoea, which are poorly specific and may account for delayed diagnosis. Organ involvement in systemic AL amyloidosis is now defined by consensus criteria, which have been updated at the 2010 meeting of the International Society of Amyloidosis ...
Considering that the patient did not fulfill diagnostic criteria for lymphoproliferative diaseases (myeloma, lymphoma or Waldenstrm's macroglubulinemia), nor for secondary malignant paraproteinemia, a diagnosis of idiopathic AL amyloidosis with biclonal gammopathy was made. Very few cases of idiopathic ...
Organ involvement in systemic AL amyloidosis isnow defined by consensus criteria, which have beenupdated at the 2010 meeting of the International Societyof Amyloidosis in Rome [Table 1] [3-5].Kidney involvement is the most frequent, found in twothirds of patients at the time of diagnosis. If...
Fifty-three patients with AL amyloidosis seen between 1976 and 1983 were treated with colchicine, and their clinical course and survival were compared with that in 29 other patients seen between 1961 and 1973. Of the variables measured, the treatment, the patient's sex, and the time interval ...
All these [stages] predict shorter survival with amyloidosis.” Table. Mayo AL Amyloidosis Staging Criteria2 Vaishali Sanchorawala, MD, expanded on the staging system, underscoring the importance of finding a diagnosis for patients as soon as possible. “Unmet needs in advanced cardiac AL ...
Long-term outcome of high-dose melphalan and autologous stem cell transplantation for AL amyloidosis J B Perz A Rahemtulla J F Apperley Bone Marrow Transplantation (2006) Autologous stem cell transplantation in primary systemic amyloidosis: the impact of selection criteria on outcome P N Mollee...