原发性胆汁性胆管炎(primary biliary cholangitis,PBC)以前称为原发性胆汁性肝硬化(primary biliary cirrhosis,PBC),是一种以肝内小胆管损伤和胆汁淤积为特点的自身免疫性肝病,其病变由自身免疫异常引起,最终可能进展为肝硬化和肝衰竭,该病具有遗传倾向。本文主要的参考文献为中华医学会肝病学分会《2021原发性胆汁性...
(PBC)——指南与进展 PBC-AIH重叠综合征 AMA阳性PBC+AIH 先有PBC,后出现AIH,多见 先有AIH后有PBC,少见 确诊为PBC者,应考虑是否存在PBC-AIH重叠 * 原发性胆汁性肝硬化概述PrimaryBiliaryCirrhosis(PBC)——指南与进展 诊断: 1.国际自身免疫性肝炎组(IAIH-G)评分或 2.ALT>5ULN; IgG≥2ULN和或ASMA阳性; ...
Primarybiliarycirrhosis(PBC)isachronicautoimmune cholestaticliverdisorderwhichhasthepotentialtoprogress tocirrhosisandeventuallyhepaticfailure(1).Thedisease progressionofpatientswithPBCinfactvariessignificantly amongpatients,includingarelativelylongasymptomatic phaseinsomepatientswhilesomehaveamorefulminate ...
目的:探讨原发性胆汁性肝硬化(primary biliary cirrhosis,PBC)患者的临床特征,为临床诊断提供思路。方法:搜集2013年1月至2015年1月中南大学湘雅二医院收治的102例原发性胆汁性肝硬化患者的临床表现、生化检查、自身抗体、肝组织病理检查结果进行回顾性分析。结果:102例PBC患者中91例(89.21%)为女性,临床表现主要为乏力...
原发性胆汁性肝硬化(Primary Biliary Cirrhosis,PBC)的诊断与治疗的诊断与治疗上海中医药大学附属曙光医院蒋健上海中医药大学附属曙光医院蒋健
原发性胆汁性肝硬化(PBC) 3) primary biliary cirrhosis 原发性胆汁性肝硬化 1. The study on expression of Toll-like receptor4 gene in peripheral blood mononuclear cells fromprimary biliary cirrhosispatients and its clinical significance; 原发性胆汁性肝硬化患者外周血单个核细胞Toll样受体4基因的表达及临...
A multicenter, controlled trial of ursodiol for the treatment of primary biliary cirrhosis. UDCA-PBC Study Group Management of primary biliary cirrhosis. The American Association for the Study of Liver Diseases practice guidelines Management of Primary Biliary Cirrhosis. ...
Keywords:malepatients;primarybiliarycirrhosis;anti-mitochondrialantibody 原发性胆汁性肝硬化(PBC)是一种与自身免疫 有关的慢性进行性胆汁淤积性肝病,其病理特征主 要是肝内中小胆管非化脓性炎性破坏,进一步可发 展为肝硬化和(或)门脉高压症。随着近年诊断技 ...
Primary biliary cirrhosis(原发性胆汁性肝硬化数据)数据摘要:The data set found in appendix D of Fleming and Harrington, Counting Processes and Survival Analysis, Wiley, 1991.中文关键词:数据挖掘,医学,原发性,胆汁性,肝硬化,英文关键词:Data mining,Medical,Primary,Biliary,Cirrhosis,数据格式:TEXT 数据...
Key words: Primary biliary cholangitis(PBC) Noninvasive cirrhosis model Hematocrit(HCT)参考文献(共19条): [1] Shah RA, Kowdley KV. Current and potential treatments for primary biliary cholangitis[J]. Lancet Gastroenterol Hepatol, 2020,5(3):306-315. [2] Yokoda RT, Carey EJ. Primary biliary...