Very long-chain fatty acids in peroxisomal disease. Adv. Exp. Med. Biol. 318: 331-340.Poulos A, Beckman K, Johnson DW, Paton BC, Robinson BS, Sharp P, et al. Very long-chain fatty acids in peroxisomal disease. Adv Exp Med Biol. 1992;318:331- 40....
Very long-chain fatty acids (VLC-FAs) with a chain longer than 22 carbons exhibit specific functions in the tissues, for example in liver homeostasis, myelin maintenance, skin barrier formation, myelin formation, retinal functions, anti-inflammation, and others. These functions are asserted by ...
Very Long Chain Fatty Acids (VLCFA)Very long-chain fatty acids (VLCFAs) are fatty acids with a chain length greater than twenty-two carbons long. VLFCAs are typically found in small amounts in mammalian tissue. VLCFAs differ in chain length, as well as location and number of double bonds...
Inherited metabolic disease Fiona Carragher, Mike Champion, in Clinical Biochemistry: Metabolic and Clinical Aspects (Third Edition), 2014 Plasma very long chain fatty acids Very long chain fatty acids, with carbon chain length ≥ 22, are exclusively metabolized by β-oxidation in peroxisomes. The ...
1.The relationship between blood very long chain fatty acids(VLCFA),1HMRS changes and the disease courses was evaluated.探讨血极长链脂肪酸(VLCFA)水平、1HMRS表现与疾病的关系。 3)very long-chain fatty acid极长侧链脂肪酸 英文短句/例句 1.Inhibitors of Biosythesis of Very Long-Chain Fatty Acids ...
We consider VLCFA to be secondary to the pathogenesis of RS, but the possible abnormalities in their levels may provide an insight into the development of this disease. CONCLUSION: Very long-chain fatty acid and carnitine levels are decreased in Rett syndrome L-Carnitine administration increased ...
1.The relationship between blood very long chain fatty acids(VLCFA),1HMRS changes and the disease courses was evaluated.探讨血极长链脂肪酸(VLCFA)水平、1HMRS表现与疾病的关系。 3)very long chain fatty acids极长链脂肪酸 4)Branched fatty acid侧链脂肪酸 5)Elovl极长链脂肪酸延伸因子 6)long-chain fa...
Childhood adrenoleukodystrophy (cALD) is a metabolic disorder in which very long-chain fatty acids (VLCFA) accumulate due to ALD protein gene defects, ultimately leading to lipotoxicity-induced neuroinflammatory demyelinating disease. Therefore, we examined VLCFA-mediated alterations in the metabolism of ...
114: Measurement of plasma very long chain fattyacids (LCFA) in children with Addison??s disease (AD)114ciprofloxacinpost-marketing surveillanceurinary tract infectionPediatric Research publishes original papers, invited reviews, and commentaries on the etiologies of diseases of children and disorders of...
1) very-long-chain fatty acides 超长链饱和脂肪酸1. Adrenoleukodystrophy is an X-linked disease , The characteristic biochemical abnormality of ALD is the accumulation of very-long-chain fatty acides(VLCFA). 肾上腺脑白质营养不良(ALD)为X-连锁隐性遗传病,生化上以超长链饱和脂肪酸蓄积为特征。