X-linked adrenoleukodystrophy: very long-chain fatty acid metabolism is severely impaired in monocytes but not in lympho- cytes. Hum Mol Genet. 2014;23:2542-50.Weber FD, Wiesinger C, Forss-Petter S, Regelsberger G, Einwich A, et al. (2014) X-linked adrenoleukodystrophy: very long-chain...
M. Dasouki, in Biomarkers in Inborn Errors of Metabolism, 2017 11.4.1 Very Long Chain Fatty Acids Elevated plasma and tissue VLCFA levels is the hallmark of almost all peroxisomal disorders especially X-ALD, which is the most common peroxisomal disorder including 85% of obligate heterozygous fema...
Very long-chain fatty acids (VLC-FAs) with a chain longer than 22 carbons exhibit specific functions in the tissues, for example in liver homeostasis, myelin maintenance, skin barrier formation, myelin formation, retinal functions, anti-inflammation, and others. These functions are asserted by ...
the levels of very long chain fatty acids (VLCFA) were shown to be elevated in CRC tissues, although the endogenous form of VLCFA has not been fully elucidated. In this study we analyzed the amount of
It is suggested that CoA esters that are poorly oxidized by the mitochondria (e.g., esters of erucic acid, of some fatty acids with trans double bonds, and of clofibric acid) may trigger the adaptation process.-Bremer, J., and K. R. Norum. Metabolism of very long-chain monounsaturated...
将“very long chain fatty acid"自动翻译成 意大利文 acido grasso a catena molto lunga Glosbe Translate 错误 Google Translate 添加示例 在上下文、翻译记忆库中将“very long chain fatty acid"翻译成 意大利文 变形干 匹配词 所有精确任何 Biochemically, X-linked ALD (X-ALD) is characterised by transport...
et al.Modulation of the very long chain fatty acid (VLCFA)formation in leek. Plant Lipid Metabolism . 1994Modulation of the very-long-chain fatty acid (VLCFA) formation - C, Schneider, et al. - 1994Modulation of the verylong-chain fatty acid (VLCFA) formation in leek - Cassagne, Bessou...
Childhood adrenoleukodystrophy (cALD) is a metabolic disorder in which very long-chain fatty acids (VLCFA) accumulate due to ALD protein gene defects, ultimately leading to lipotoxicity-induced neuroinflammatory demyelinating disease. Therefore, we examined VLCFA-mediated alterations in the metabolism of ...
This study provides the theoretical foundation for the study of fatty acid metabolism in the process of lactation. 展开 关键词: Dairy goat Elongase of very long chain fatty acids 6(ELOVL6 Tissue expression Over expression 被引量: 2 年份: 2014 ...
Very-long-chain fatty acids (VLCFAs; 22–26 carbons) are essential biological components, which are incorporated in triacylglycerol molecules, sphingolipids, cuticle or waxes1. VLCFAs such as erucic acid, as well as VLCFA-derived products such as very-long-chain fatty alcohols (VLCFAlc) (for ...