We examined a large national registry of patients with CVID to better characterize this population and understand how the presence of enteropathy influences nutritional status, patient function, and the risk of additional non-infectious disorders in CVID patients. We also sought to illustrate the range...
Impact of pulmonary complications on quality of life in the USIDNET registry Purpose The United States Immunodeficiency Network (USIDNET) patient registry was used to characterize the presentation, genetics, phenotypes, and treatmen... Rohr,Kaileen,Yu,... - 《Journal of Clinical Immunology》 被引量...
Adenosine Deaminase (ADA)–Deficient Severe Combined Immune Deficiency (SCID) in the US Immunodeficiency Network (USIDNet) RegistryAdenosine deaminase–deficient severe combined immune deficiencyADA-SCIDimmunodeficiencyhematopoietic stem cell transplantgene therapyUS Immunodeficiency Network (USIDNet)...
In the USIDNET Registry, we describe infection frequency and infection-related mortality in patients with XLA and their relationship to age of diagnosis and treatment initiation. Among the 231 XLA patients enrolled in the Registry, respiratory infections ( N =203, 88%) were the most commonly ...
Cunningham-Rundles, CharlotteSpringer USJournal of Clinical ImmunologyFeuille EJ, Anooshiravani N, Sullivan KE, Fuleihan RL, Cunningham-Rundles C. Autoimmune cytopenias and associated conditions in CVID: a report from the USIDNET Registry. J Clin Immunol (2018) 38(1):28-34. doi:10.1007/ s...
OR064 Ocular manifestations in primary immunodeficiency (PID) patients within the us immunodeficiency network (USIDNET) registryRationalePrimary immunodeficiency (PI) diseases can be treated effectively, especially if recognized early. We studied patients referred to a large immunodeficiency program for a ...
Complications Associated with Underweight Primary Immunodeficiency Patients: Prevalence and Associations Within the USIDNET RegistryPrimary immunodeficiencycommon variable immunodeficiencyfailure to thriveobesityunderweightNational Health and Nutrition Examination Survey (NHANES)...
Infectious and Non-infectious Pulmonary Complications of Primary Immunodeficiency Diseases in the USIDNET Registrydoi:10.1016/j.jaci.2017.12.076Rohr, KaileenYu, Joyce EJournal of Allergy & Clinical Immunology
Here, we report prevalence of autoimmune cytopenias in CVID from the USIDNET Registry and compare the demographics and clinical features of patients with and without this complication.Feuille, Elizabeth J.Anooshiravani, NiloofarSullivan, Kathleen E.Fuleihan, Ramsay L.Cunningham-Rundles, Charlotte...
An Example of How the USIDNET Registry Can Empower ResearchHernandezTrujilloVivianAaaai