The urea cycle and related enzymes in human erythrocytes were studied. 1. 1. Arginine, ornithine and citrulline were found in small amounts but ornithine citrulline transferase and carbamyl phosphate synthetase were not found. 2. 2. Concentrations of the detected enzymes were 1/30 to 1/120 of...
UREA CYCLE ENZYMES AND OROTIC ACID (OA) IN REYE??S SYNDROME (RS)To ascertain cerebral metabolic responses to hypoglycemia with superimposed hypoxia, newborn rats were given regular insulin (30 u/kg s.c.). Animals were observed for up to 2 hrs with no ill effects, inspite of blood ...
1. Time course of urea cycle enzymes in leukocytes. Carbamylphosphate synthetase system contained 0.510 mg protein; ornithine transcarbamylase, 0.187 mg protein; argininosuccinate synthetase and lyase, 0.620 mg protein, and arginase, 0.097 mg protein. Carbamyl Phosphate Synthetase in Leukocytes 0.03, ...
urea enzymes 【医】 脲酶, 尿素酶 urea bacterium 尿素细菌 urea seeding 尿素催化 benzoylene urea 亚苯甲酰基脲 allyl urea 烯丙基脲 diacetyl urea 二乙酰脲 相似单词 urea n. 尿素 cycle n. 1.循环,周期 2.自行车,摩托车 3.整套,整个系列(如机器的运转) v.[I] 1.骑自行[摩托]车,骑自...
Urea cycle enzymesCurrent methodologies for the assessment of urea cycle (UC) enzymatic activity are insufficient to accurately evaluate this pathway in biological specimens where lower UC is expected. Liver cell lines, including HepaRG, have been described to have limited nitrogen fixation through the...
very sensitive to ammonia. Ammonia intoxication produces a comatose state. Cells get rid of excess ammonia by the reductive amination of α−ketoglutarate to form glutamate by glutamate dehydrogenase and the conversion of glutamate into glutamine by glutamine synthetase. Both of these enzymes are...
Urea is generated by the urea cycle enzymes, which are mainly in the liver but are also ubiquitously expressed at low levels in other tissues. The metabolic process is altered in several conditions such as by diets, hormones, and diseases. Urea is then eliminated through fluids, especially urin...
ACER-001 for Urea Cycle Disorders (UCDs)Urea Cycle Disorders (UCD) The urea cycle is a component of protein metabolism that takes place primarily in a person’s liver. When the body breaks down protein, ammonia is produced, which is toxic. Enzymes in the urea cycle are responsible for the...
Isolated hepatocyte transplantation in an infant with a severe urea cycle disorder. Neurologic outcome in children with inborn errors of urea synthesis. Outcome of urea-cycle enzymopathies Induction of ornithine-urea cycle enzymes and nitrogen metabolism and excretion in rainbow trout (Oncorhynchus mykiss...
1. Time course of urea cycle enzymes in leukocytes. Carbamylphosphate synthetase system contained 0.510 mg protein; ornithine transcarbamylase, 0.187 mg protein; argininosuccinate synthetase and lyase, 0.620 mg protein, and arginase, 0.097 mg protein. Carbamyl Phosphate Synthetase in Leukocytes 0.03, ...