signs and symptomspurpuramacroglossiadiagnosisdrug therapytreatmentoutcomeBackground. Systemic amyloidosis is a rare disorder which usually occurs in aged persons and has a poor prognosis. Systemic amyloidosis can be primary, occasionally associated with multiple myeloma, or secondary, associated with another...
"The relationship between AL amyloidosis and MGUS is less clear, but some studies suggest that the risk of developing AL amyloidosis may be increased in patients with MGUS. It is important for patients with these conditions to undergo regular monitoring and evaluation for signs of AL amyloidosis, ...
European Society of Haematology and International Society of Amyloidosis (EHS-ISA) [42, 43] Workup The NCCN recommendation for diagnostic evaluation includes [29] : Detailed history and physical examination Evaluation of orthostatic vital signs The recommended laboratory work-up includes [29] : ...
To determine the metabolic fate of factor X in primary amyloidosis associated with factor X deficiency, we examined the pathways of its catabolism in a man with this syndrome. Intravenous infusion of human or bovine131I-labeled factor X established a triphasic plasma clearance pattern for factor ...
NCCN Guidelines Version 2.2023 Systemic Light Chain Amyloidosis NCCN Guidelines Index Table of Contents Discussion NCCN Systemic Light Chain Amyloidosis Panel Members Summary of Guidelines Updates Initial Diagnostic Workup (AMYL-1) Clinical Findings and Primary Treatment (AMYL-2) Systemic Light Chain ...
Brucellosis is a systemic infection involving many organs and tissues. The musculoskeletal system is one of the most commonly affected. The disease can pre... H Turan,K Serefhanoglu,E Karadeli,... - 《International Journal of Infectious Diseases》 被引量: 16发表: 2009年 Systemic amyloidosis ...
A 13-year-old Iranian girl, who presented with ecchymosis and swelling signs around both eyes (peri-orbital), especially on the left side, was admitted in Pediatric Rheumatologic ward, Mofid Children,s Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. The swelling and ecchym...
(and related disorders) HCV sialadenitis Sjögren's syndrome (and rarely bilateral non-Hodgkin's lym- phoma) IgG4 related disease Sarcoidosis Sarcoidosis Chronic non-specific sialadenitis Sialosis Xanthogranulomatous sialadenitis Pneumoparotitis Amyloidosis Iodine containing contrast media and radioactive ...
Liver transplantation as a specific treatment of transthyretin amyloidosis was first performed in 1990. The rationale for this treatment was that removal o... Benson,D Merrill - 《Muscle & Nerve》 被引量: 77发表: 2013年 Abstract 4347: Medulloblastoma comprises four distinct diseases Prior attempts...
Multicentric Castleman's disease (MCD) is a rare systemic lymphoproliferative disorder with too few patient series reported in the literature to have a clear idea about the etiology, outcome and the best treatment available. Systemic reactive amyloidosis is a very rare complication of MCD and its ...