Rasmussen综合征3例临床病理观察 Rasmussen综合征(rasmussensyndrome,RS),又称Rasmussen脑炎,是一种儿童期起病、致使一侧大脑半球皮质萎缩的进行性多灶性脑病[1]。临床表现为局灶性难治性癫痫(20%)、部分性癫痫持续状态(epilepsiapartialiscontinua,EPC)(50%)和进行性神经功...
3 Kim SJ, Park YD, Pillai JJ, et al. A Longitudinal MRI Study in Children with Rasmussen Syndrome[J]. PediatrNeurol, 2002, 27 (4) :280-282. 4 Fiorella DJ, Provenzale JM, Coleman RE, et al. 18F-Fluorodeox- yglucose positron emission tomography and MR imaging findings in Rasmussen en...
Rasmussen's syndrome (chronic encephalitis with epilepsy) is a rare neurological disorder characterised by progressive dysfunction of one cerebral hemisphere. Clinical and radiological features of the syndrome include intractable epilepsy, cognitive and motor decline, progressive unilateral cortical atrophy and...
8. Carlos A Pardo, Rima Nabbout, Aristea S.Galanopoulou mechanisms of epileptogenesis in pediatric epileptic syndromes:Rasmussen encephalitis, Infantile spasms, and Febrile infection-related epilepsy syndrome (FIRES).Neurotherapeutics, 2014, 11(4):297-310. 9. Sophia Varadkar, Christian G Bien, Ca...
Rasmussen’s syndrome (also known as Rasmussen’s encephalitis) appears to be an autoimmune process that causes one hemisphere of the brain to become inflamed and deteriorate. Inflammation may stop without treatment, but the damage is irreversible. Rasmussen’s syndrome is associated with intractable ...
Pre-and postsurgical cognitive trajectories and quantitative MRI changes in Rasmussen syndrome. Epilepsia, 2018, 59(6): 1210-1219. 12. Schwab N, Bien CG, Waschbisch A, et al. CD8+ Tcell clones dominate brain infiltrates in Rasmussen encephalitis and persist in the periphery. Brain, 2009, ...
英文: Objective: Sicca syndrome (SS) also named Sjogren s Syndrome.中文: 干燥综合征(Sicca syndrome,SS)又名斯耶格伦综合征(Sjogren’s SyndromeSS),最早是由瑞典眼科医师 Henrik Sjogren在1933年提出的,当时定义为干燥性角膜炎、口干燥症和类风湿关节炎的三联征。
【关键词】 Rasmussen 综合征 临床表现 磁共振成像Clinical Manifestations and MRI features of Rasmussen SyndromeZHOU Xiaoliang,HUANG Biao,LIU Yongjian,et al.Department of Radiology ,Longggang Central Hospital of Shenzhen City. Shenzhen 518116,P. R. China【Abstract】 Objective To analyze the clinical ...
Rasmussen综合征是一种散发的、起病于儿童期的病因未明的疾病。本病早期多表现为部分性癫痫或癫痫持续状态，其影像学表现为进行性一侧半球萎缩及T2和(或)FLAIR异常信号。药物治疗无明显效果，疾病发展到晚期将导致病儿偏瘫及智能障碍。抗癫痫药物疗效差，激素冲击治疗或免疫球蛋白治疗，部分病人有短时的缓解作用。癫痫不...