Propionyl CoA carboxylase is a dodecameric enzyme consisting of multiple copies of alpha and beta subunits encoded by the PCCA and PCCB genes. Mutations in either PCCA or PCCB can cause the disease. PA is categorized as a rare disease and accessing patients' cells to study the disease has ...
The mRNA used in the present invention, when administered in vivo, is human propionyl CoA carboxylase alpha (PCCA) and / or human propionyl CoA carboxylase beta (PCCB), and its isoforms, functional fragments thereof, and PCCA and / or PCCB. Encodes a fusion protein containing. The mRNAs of...
Propionic acidemia (PA) is an autosomal recessive metabolic liver disease caused by defects in propionyl CoA carboxylase. Propionyl CoA carboxylase is a dodecameric enzyme consisting of multiple copies of alpha and beta subunits encoded by the PCCA and PCCB genes. Mutations in either PCCA or PCCB ...
Crystal structure of the beta-subunit of acyl-CoA carboxylase: structure-based engineering of substrate specificity Biochemistry, 43 (2004), pp. 14027-14036 View in ScopusGoogle Scholar [13] T. Ohura, J.P. Kraus, L.E. Rosenberg Unequal synthesis and differential degradation of propionyl CoA car...
Propionyl CoA carboxylase Propionyl coenzymeA propionyl-CoA Propionyl-CoA carboxylase Propionyl-CoA Carboxylase, Alpha Subunit Propionyl-CoA Carboxylase, Beta Subunit propionylglycine Propios Propithecus propitiable propitiate propitiated propitiates propitiating propitiatingly propitiation propitiations propitiatious...
The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit...
glycerol kinase; GPD1, glycerol-3-phosphate dehydrogenase 1; GPD2, glycerol -3-phosphate dehydrogenase 2; ACSS3, acyl CoA synthetase short chain family member 3; PCCA,propionyl CoA carboxylasealpha; PCCB,propionyl CoA carboxylasebeta; MCEE, methylmalonyl CoA epimerase; MUT, methylmalonyl CoA mutase...
carboxylase羧化酶; 羧化酶; 羧酶; 羧酶 methylmalonyl CoA甲基丙二酸单酰辅酶A beta carboxylase【医】 β-羧酶 coa=Change of Assignment 改变任务 Committee on Accreditation 鉴定委员会([美] ALA) CoA【化】 辅酶A 【医】 辅酶A COA=Change of Assignment 改变任务 Committee on Accreditation 鉴定委员会(...
PCCA Antibody is a Rabbit Polyclonal Antibody against PCCA.应用类型 WB免疫原 PCCA来源宿主 兔反应性 人,小鼠,大鼠保存建议 建议收到该Propionyl-CoA Carboxylase Alpha Subunit (PCCA) Antibody产品后,储存温度为-20°C。避免重复冻融其他 Abbexa总部位于英国剑桥的剑桥科学园,是一家专业的全球抗体供应商和蛋白...
产品名称:Propionyl-CoA carboxylase beta chain, mitochondrial ELISA Kit 检测范围:0.156-10 ng/mL 保存条件:2-8℃低温保存 保质期:6个月,所有试剂盒均提供批次。 试剂盒成分:酶标板,试剂,标准品等。 选型: 产品规格:96T/48T 96T指可以做94个标本-2个标准对照-84个样本 ...