carboxylase羧化酶; 羧化酶; 羧酶; 羧酶 methylmalonyl CoA甲基丙二酸单酰辅酶A beta carboxylase【医】 β-羧酶 coa=Change of Assignment 改变任务 Committee on Accreditation 鉴定委员会([美] ALA) CoA【化】 辅酶A 【医】 辅酶A COA=Change of Assignment 改变任务 Committee on Accreditation 鉴定委员会(...
网络丙酰辅酶A羧化酶;脢羧化脢
Propionyl-CoA carboxylase Propionic acidemia Methylcitrate 3-hydroxypropionate 1. Introduction Propionyl-CoA carboxylase (PCC, E.C. 6.4.1.3) catalyzes the carboxylation of propionyl-CoA with bicarbonate producing methylmalonyl-CoA which is then converted to succinyl-CoA, an intermediate in the tricarboxylic...
(redirected fromPropionyl CoA carboxylase) pro·pi·o·nyl-CoA car·box·yl·ase an enzyme that catalyzes the reaction of propionyl-CoA with CO2and ATP to produce ADP, orthophosphate, andd-methylmalonyl-CoA; a biotin-dependent enzyme; an inherited deficiency of this enzyme will lead to propionic...
Propionyl-CoA carboxylase of Myxococcus xanthus : catalytic properties and function in developing cells. Arch Microbiol. 1998; 170 :179–184. doi: 10.1007/s002030050631. [ Cross Ref ]Kimura, Y., Kojyo, T., Kimura, I., and Sato, M. (1998) Propionyl- CoA carboxylase of Myxococcus xanthus:...
产品名称:Propionyl-CoA carboxylase beta chain, mitochondrial ELISA Kit 检测范围:0.156-10 ng/mL 保存条件:2-8℃低温保存 保质期:6个月,所有试剂盒均提供批次。 试剂盒成分:酶标板,试剂,标准品等。 选型: 产品规格:96T/48T 96T指可以做94个标本-2个标准对照-84个样本 ...
网络羧化酶缺乏 网络释义 1. 羧化酶缺乏 如丙酰辅酶A羧化酶缺乏(propionyl CoA carboxylase deficiency) 和多种羧化酶缺乏(multiple carboxylase deficiency)症,两者 … www.wiki8.com|基于2个网页
Propionyl-CoA carboxylase propionyl Coenzyme A carboxylase, alpha polypeptide Identifiers Symbol PCCA Entrez 5095 HUGO 8653 OMIM 232000 RefSeq NM_000282
ORIGINAL ARTICLEPropionyl-CoA carboxylase pcca-1 and pccb-1 gene deletionsin Caenorhabditis elegans globally impair mitochondrial energymetabolismKimberly A. Chapman 1,2 & Julian Ostrovsky 1 & Meera Rao 1 & Stephen D. Dingley 1 &Erzsebet Polyak 1 & Marc Yudkoff 1,3 &...
Small amounts of alloisoleucine appeared in plasma. Propionyl-CoA carboxylase deficiency was suggested by this metabolite pattern and demonstrated in cultured fibroblasts. 展开 关键词: Ketotic hyperglycinemia syndrome Propionyl-CoA carboxylase deficiency Isoleucine metabolites ...