The binding of acyl-CoA substrate to the carboxylase appears to involve the 3′-phosphate, adenine, and pantoyl moieties of the subsrate. Propionyl-CoA carboxylase is protected from p- chloromercuribenzoate inhibition by propionyl-CoA, whereas, ATP-MgCl 2 facilitates this inhibition....
Propionyl-CoAcarboxylasehas α andβ subunits. In immunotitration, neither pccA nor pccBC may contain cross-reacting material (CRM). Among patients in the Mut0 group of methylmalonyl-CoAmutase, immunotitration studies have revealed some to have some CRM, albeit reduced, whereas others have none....
Significantly, propionyl-CoA carboxylase was clearly reduced in both parents' fibroblasts. Therefore, ‘ketotic hyperglycinemia’ is actually propionyl-CoA carboxylase deficiency, and this explains the protein intolerance and the remarkable similarity of this condition to methylmalonicaciduria. Finally, ...
Propionyl-CoA carboxylase propionyl Coenzyme A carboxylase, alpha polypeptide Identifiers Symbol PCCA Entrez 5095 HUGO 8653 OMIM 232000 RefSeq NM_000282
沪江词库精选propionyl CoA carboxylase是什么意思、英语单词推荐 丙酰辅酶A羧化酶 相似短语 propionyl CoA carboxylase 丙酰辅酶A羧化酶 propionyl iodide 丙酰碘 acetyl CoA carboxylase 乙酰辅酶A羧化酶 propionyl salicylic acid 丙酯基水杨酸 propionyl fluoride 丙酰氟 propionyl bromide 丙酰溴 propionyl...
PCCA 来源宿主 兔 反应性 人,小鼠,大鼠 保存建议 建议收到该Propionyl-CoA Carboxylase Alpha Subunit (PCCA) Antibody产品后,储存温度为-20°C。避免重复冻融 其他 Abbexa总部位于英国剑桥的剑桥科学园,是一家专业的全球抗体供应商和蛋白质供应商,致力于为生命科学、药物开发和生物技术领域的科学家和研究者提供最佳...
机译:酰基-CoA定量以及通过天然和茄形青枯菌丙酰基-CoA合成酶的过表达对大肠杆菌聚酮化合物底物的影响。 6. Propionyl Coenzyme A (Propionyl-CoA) Carboxylase in Haloferax mediterranei: Indispensability for Propionyl-CoA Assimilation and Impacts on Global Metabolism [O] . Jing Hou, Hua Xiang, Jing ...
英文别名: propionyl CoA carboxylase (ATP-hydrolyzing)中文名: 中文别名: CBNumber: CB31344977 分子式: 分子量: 0 MOL File: Mol file 化学性质 安全信息 用途 供应商 0 propionyl CoA carboxylase (ATP-hydrolyzing)化学性质 安全信息propionyl CoA carboxylase (ATP-hydrolyzing)性质、用途与生产工艺 propionyl ...
CAS号: 9023-94-3 英文名: propionyl-CoA carboxylase 英文别名: propionyl-CoA carboxylase 中文名: propionyl-CoA carboxylase 中文别名: CBNumber: CB11313432 分子式: 分子量: 0 MOL File: Mol file 化学性质 安全信息 用途 供应商 2 propionyl-CoA carboxylase化学性质 ...
(redirected fromPropionyl CoA carboxylase) pro·pi·o·nyl-CoA car·box·yl·ase an enzyme that catalyzes the reaction of propionyl-CoA with CO2and ATP to produce ADP, orthophosphate, andd-methylmalonyl-CoA; a biotin-dependent enzyme; an inherited deficiency of this enzyme will lead to propionic...