Alstr??m syndrome is a rare autosomal recessive disorder with dilated cardiomyopathy in 60% of patients. Despite the frequency of cardiac involvement in Alstr??m syndrome, conduction system abnormalities or arrhythmias have not been characterized previously. We report two siblings with Alstr??m ...
The extent of cardiac abnormalities varies based on the degree of infiltration and results in increased ventricular wall thickness, chamber dilatation, and disruption of the conduction system. These changes often lead to the development of heart failure, atrioventricular (AV) block, and ventricular ...
diseases such as optical coherence tomography [36], powerful electrophysiological, mechanical, and histological approaches to characterize heart development, cardiac tissue properties, and structure in theDrosophilaheart have emerged as a pioneering model system in basic, genetic, and molecular studies of ...
Inherited cardiomyopathies as a collective group, are relatively common cardiac disorders. Individuals can present with symptoms of chest pain, dyspnoea, palpitations, syncope and with progressive heart failure or sudden cardiac death. Genetic mutations
Nomura H, Hizawa K. Histopathological study of the conduction system of the heart in Duchenne progressive muscular dystrophy. Acta Pathol Jpn. 1982;32(6):1027–33. CASPubMedGoogle Scholar Yotsukura M, Sasaki K, Kachi E, Sasaki A, Ishihara T, Ishikawa K. Circadian rhythm and variability of...
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The Cardima Revelation T-Flex system (55掳C for 60s per pole) was used to block conduction into left and right sided pulmonary veins and perform roof and mitral isthmus lines. Patients with PERAF and redo procedures underwent right ... None - 《Journal of Interventional Cardiac Electrophysiology...
of presentation and severity of symptoms.5 Cardiac features include concentric ventricular hypertrophy, dilated cardiomyopathy (DCM) and congestive heart failure.6–8 Cardiac conduction features include atrioventricular and bundle branch blocks.9 When mitochondrial disease primarily affects only the heart, ...
Cardiomyopathies are a varied group of heart diseases that are characterized by abnormalities of the heart muscle. Although these generally exclude those secondary to coronary artery disease, hypertension, congenital, valvular, or pericardial pathology,
Nondepolarizing Neuromuscular Conduction Blocking Agents Nondepolarizing neuromuscular conduction blocking agents (NMBAs), which do not induce depolarization, are a key component of medical procedures, especially in the context of endotracheal intubation [1]. They are divided into 2 main groups based on...