棕榈蛋白酯酶 1 前体,指认 [蓖麻] 翻译结果4复制译文编辑译文朗读译文返回顶部 palmitoyl-蛋白质thioesterase1前体,假定[ricinus确定] 翻译结果5复制译文编辑译文朗读译文返回顶部 Palmitoyl蛋白质thioesterase 1个前体,想像(蓖麻communis) 相关内容 a需求不断增长 The demand grows unceasingly[translate] ...
中文名称: 棕榈酰蛋白硫酯酶1(PPT1)重组蛋白 中文同义词: 棕榈酰蛋白硫酯酶1(PPT1)重组蛋白 英文名称: Recombinant Palmitoyl Protein Thioesterase 1 (PPT1) 英文同义词: Recombinant Palmitoyl Protein Thioesterase 1 (PPT1) CAS号: 分子式: 分子量: 0 EINECS号: 信息错误报告 您的Email: 按国家浏览...
Neuronal ceroid lipofuscinoses represent the most common childhood neurodegenerative storage disorders. Infantile neuronal ceroid lipofuscinosis (INCL) is caused by palmitoyl protein thioesterase-1 (PPT1) deficiency. Although INCL patients show signs of abnormal neurotransmission, manifested by myoclonus and se...
Palmitoyl-acyl carrier protein (ACP) thioesterase and the evolutionary origin of plant acyl-ACP thioesterases. A. 1995. Palmitoyl-acyl Carrier Protein (ACP) Thioesterase and the Evolutionary Origin of Plant Acyl-ACP Thioesterases. Plant Cell., 7: 359-371... Jones,A. - 《Plant Cell》 被引...
R. Protein depalmitoylases. Crit. Rev. Biochem. Mol. Biol. 53, 83–98 (2018). Article CAS PubMed Google Scholar Kong, E. et al. Dynamic palmitoylation links cytosol-membrane shuttling of acyl-protein thioesterase-1 and acyl-protein thioesterase-2 with that of proto-oncogene H-ras ...
Palmitoyl-protein thioesterase (PPT) is a lysosomal enzyme that removes fatty acids bound in thioester linkage to cysteine residues in fatty acylated proteins (1–4). Mutations in the PPT gene that affect enzyme activity cause a recessively inherited lysosomal storage disorder, infantile neuronal cero...
pdf1, a palmitoyl protein thioesterase 1 Ortholog in Schizosaccharomyces pombe: a yeast model of infantile Batten disease. Infantile Batten disease is a severe neurodegenerative storage disorder caused by mutations in the human PPT1 (palmitoyl protein thioesterase 1) gene, whic... Steve,K,Cho,......
Methods for assaying palmitoyl protein thioesterase 1 and tripeptidyl peptidase activity in dried blood spots for detection of neuronal ceroid lipofuscinos... The present disclosure provides assays for lysosomal enzymes, specifically palmitoyl protein thioesterase 1 (PPT1) and tripeptidyl peptidase 1 (TPP...
While inactivating mutations in the CLN1 gene, encoding palmitoyl‐protein thioesterases‐1 (PPT1), cause infantile NCL (INCL), those in the CLN3 gene, encoding a protein of unknown function, underlie juvenile NCL (JNCL). PPT1 depalmitoylates S‐palmitoylated proteins (constituents of ceroid)...
The defective gene behind the INCL disease, CLN1, encodes for palmitoyl protein thioesterase 1 (PPT1) [3]. It consists of 306 amino acids, including a signal sequence of 26 amino acids and three N-linked glycosylation sites. The enzyme is transported into lysosomes of non-neuronal cells by...