Singh H, Brogan M, Johnson D, Poulos A: Peroxisomal beta-oxidation of branched chain fatty acids in human skin fibroblasts. J Lipid Res 1992, 33:1597-1605.Singh H, Brogan M, Johnson D, Poulos A (1992) Peroxisomal ß-oxidation of branched chain fatty acids in human skin fibroblasts. J...
Peroxisomal beta-oxidation is specialized in that it metabolizes very long-chain fatty acids, which are composed of 24 to 26 carbon units. Processing of these molecules proceeds similarly to mitochondrial beta-oxidation; however, some enzymatic steps differ and are discussed below. Alpha oxidation of...
Metabolism of branched-chain amino acids in maple syrup urine disease. Eur J Pediatr. 1997;156(Suppl 1):S62-6.Schadewaldt P, Wendel U (1997) Metabolism of branched- chain amino acids in maple syrup urine disease. Eur J Pediatr 156[Suppl 1]:S62±S66...
The in vitro omega-oxidation of phytanic acid and other branched chain fatty acids by mammalian liver. Scand. J. Clin. Lab. Invest. 22: 224-230.Try, K. 1968. The in vitro omega-oxidation of phytanic acid and other branched chain fatty acids by mammalian liver. Scand. J. Clin. Lab ...
3. 3. Addition of camitine esters of fatty acids (C 6–C 16), succinate, pyruvate, or α-ketoglutarate inhibited the oxidation of the branched chain α-keto acids, especially in a high-energy state (no ADP added). In heart mitochondria the addition of ADP (low-energy state) decreased ...
9. Which pathway is used for degradation of amino acids like Leucine, Isoleucine, and Valine? A. Glycolysis B. Pentose phosphate pathway C. Similar to fatty acid oxidation D. Urea cycle E. Oxidative phosphorylation Answer: C 10. What is a common outcome of genetic diseases related to defects...
Plasma levels of branched-chain amino acids (BCAA) are consistently elevated in obesity and type 2 diabetes (T2D) and can also prospectively predict T2D. However, the role of BCAA in the pathogenesis of insulin resistance and T2D remains unclear. To identify pathways related to insulin resistance...
15 DIFFERENTIALLY IMPAIRED OXIDATION OF BRANCHED- CHAIN AMINO ACIDS I N MAPLE SYRUP URINE DISEASE (MSUD) FIBHOBLASTS P e t e r S c h a d e w a l d t and Udo wendel' (spo and n. K i by nde H.-J. rklin i k Br? C m,e r), I n Univ. st o . f P h y s i o ...
The stereochemistry of the alpha-oxidation of 3-methyl-branched fatty acids was studied in rat liver. R- and S-3-methylhexadecanoic acid were equally well ... K Croes,M Casteels,D Noubhani-M,... - 《Journal of Lipid Research》 被引量: 0发表: 1999年 Free fatty acids in obesity and...
The interactions between fatty acid oxidation and the oxidation of the 2-oxo acids of the branched chain amino acids were studied in the isolated Langendorff-perfused heart. 2-Oxoisocaproate inhibited the oxidation of oleate, but 2-oxoisovalerate and 2-oxo-3-methylvalerate did not. This differen...