Neonatal Marfan syndrome (nMFS) is the rare and severe form of this connective tissue disorder with poor outcome due to progressive valvular insufficiency. We describe a case of nMFS suspected in utero, by fetal echocardiography, due to marked dilatation of both great arteries, which is the first...
Marfan syndrome (MFS) is a disorder of connective tissue structure and function, with a reported incidence of approximately 1 in 5000 individuals [1]. With no predilection for gender or ethnicity the UK prevalence is in the region of 10,000. In 1896, Professor Antoine Bernard-Jean Marfan, fo...
Diseases of the descending aorta have emerged as a clinical issue in Marfan syndrome following improvements in proximal aorta surgical treatment and the consequent increase in life expectancy. Although a role for hemodynamic alterations in the etiology of descending aorta disease in Marfan patients has ...
Operative Preparation of the Patient for Heart Surgery: Airway and Ventilation, Vascular Access and Monitoring Airway and ventilation management are key components in the perioperative management of patients with congenital heart disease. Diverse cardiovascular path... S Ullah,LM Zabala - Springer London...
The cardiovascular complications of the Marfan syndrome are principally responsible for the reduced life expectancy of patients with this disorder.' Aneurysmal dilatation of the aortic root leads to progressive aortic regurgitation and predisposes to aortic rupture. Dissection of the proximal aorta and aneu...