alpha#-mannosidosis in the human is an autosomal recessive lysosomal storage disease caused by a deficiency of lysosomal #alpha#-D-mannosidasea actvity. Lysosomal #alpha#-D-mannosidase is involved in the catabolism of N-linked glycoproteins through the sequential degradation of high-mannose, ...
Cat Lysosomal alpha-mannosidase (MAN2B1) ELISA Kit是MyBioSource品牌高品质试剂盒产品,多种产品规格满足不同用户的实验需求,以更简便的方式助力客户更好的结果
英文别名: Lysosomal alpha-mannosidase (MAN2B1)中文名: 中文别名: CBNumber: CB613735328 分子式: 分子量: 0 MOL File: Mol file 化学性质 安全信息 用途 供应商 1 Lysosomal alpha-mannosidase (MAN2B1)化学性质 安全信息Lysosomal alpha-mannosidase (MAN2B1)性质、用途与生产工艺 Lysosomal alpha-mannosidase (...
MAN2B1 (Lysosomal alpha-mannosidase, Laman, Lysosomal Acid alpha-mannosidase, Mannosidase alpha Class 2B Member 1, Mannosidase alpha-B, LAMAN, MANB) 供应商 MyBioSource 产品货号 MBS648521 产品报价 ￥询价/0.05mg ￥询价/5x0.05mg ￥询价/其它规格 ...
(redirected fromlysosomal) Thesaurus Medical Encyclopedia Related to lysosomal:Lysosomal enzymes ly·so·some (lī′sə-sōm′) n. A membrane-bound organelle in the cytoplasm of most cells containing various hydrolytic enzymes that function in intracellular digestion. ...
中文名称:Human Lysosomal alpha-mannosidase(MAN2B1) ELISA kit 中文同义词:人溶酶体Α甘露糖苷酶(MAN2B1)ELISA KIT 英文名称:Human Lysosomal alpha-mannosidase(MAN2B1) ELISA kit 英文同义词:Human Lysosomal alpha-mannosidase(MAN2B1) ELISA kit CAS号: ...
5) 1,2-alpha-mannosidase α-1,2-甘露糖苷酶 1. Bioinformatic analysis of a putative 1,2-alpha-mannosidase in Magnaporthe grisea; 稻瘟病菌一个假定的α-1,2-甘露糖苷酶生物信息学分析6) mannosidase ['mænəsideis] 甘露糖苷酶 1. By introducing and localiz-ing mannosidases and ...
MAN2B1 codes for lysosomal α-mannosidase (LAMAN = MAN2B1, EC 3.2.1.24), the enzyme deficient in alpha-mannosidosis (MIM# 248500) [39]. The c.2402dup pathogenic variant, which we have identified in patient P13, had already been reported in 2012, together with 82 other alpha-mannosido...
Y. Gotoda, N. Wakamatsu, H. Kawai, Y. Nishida, T. Matsumoto Missense and nonsense mutations in the lysosomal alpha-mannosidase gene (MAN B) in severe and mild forms of alpha-mannosidosis Am. J. Hum. Genet., 63 (1998), pp. 1015-1029 ...
Nebes VL, Schmidt MC (1994) Human lysosomal alpha-mannosidase: isolation and nucleotide sequence of the full-length cDNA. Biochem Biophys Res Commun. Apr 15;:239-245.Human lysosomal alpha-mannosidase: isolation and nucleotide sequence of the full length cDNA - Nebes, Schmidt - 1994 () ...