Lysogb3 1.2 Synonyms globotriaosyl lysosphingolipid; GLOBOTRIAOSYLSPHINGOSINE; Globotriaosylsphingosine from porcine blood; lyso-CeraMide Trihexoside (lyso-CTH, Globotriosyl sphingosine) Porcine; Lyso-Globotriaosylceramide (d18:1); α-d-gal-(1→4)-β-d-gal-(1→4)-β-d-glc-1→o-sphing...
lysosomal storage disease caused by mutations in the 伪-galactosidase A gene ( GLA ) leading to deficiency of 伪-galactosidase A and ultimately in progressive glycosphingolipid accumulation, especially globotriaosylceramide (Gb3) and its deacylated derivative globotriaosylsphingosine (Lyso-Gb3). ...
Lyso GB3 (synthetic) Globotriaosylsphingosine Data Hygroscopic No Light Sensitive No Molecular Formula C36H67NO17 Percent Composition C 55.02%, H 8.59%, N 1.78%, O 34.61% Purity >99% Stability 1 Year Storage Temperature -20°C CAS Number ...
Lyso GB3-d7 产品属性本产品采购属于商业贸易行为 市场价格:电议 产品型号: 更新时间:2024/1/2 10:25:37 生产地:美洲 访问次数:1238次 公司名称:MedChemExpress 进入厂商展台 企业档案 MedChemExpress 第8年证营业执照已上传 企业类型:生产商 公司地址:上海上海...
英文名称 Lyso GB3-d7 生化机理 Lyso GB3-d 7 is deuterium labeled Lyso GB3. 储存温度 -20°C储存 运输条件 超低温冰袋运输 产品介绍 Lyso GB3-d 7 is deuterium labeled Lyso GB3. In Vitro Stable heavy isotopes of hydrogen, carbon, and other elements have been incorporated into drug mo...
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Lyso-Gb3 also modified the bacterial composition of the human colon microbiota suspension, increasing bacterial counts of, among others. Finally, lyso-Gb3 modified the formation of short-chain fatty acids, leading to a striking decrease in butyrate concentration. Lyso-Gb3 modifies the biology of ...
Lyso-Gb3 as a biomarker for renal and cardiac involvement in Fabry disease: An analysis from the Fabry Outcome Survey (FOS)doi:10.1016/j.ymgme.2021.11.272U. RamaswamiG. AltarescuM. FullerK. NichollsG. Pintos-MorellJ. TorrasJ. Botha...
Lyso-Gb3 indicates that the Alpha-Galactosidase A mutation D313Y is not clinically relevant for Fabry Disease. JIMD Rep 2013;7:99-102.Niemann M, Rolfs A, Giese A, Mascher H, Breunig F, Ertl G, Wanner C, Weidemann F. 2013. Lyso-Gb3 indicates that the alpha-galactosidase A mutation...