l-2-hydroxyglutaric aciduria (l-2-HGA) is a neurometabolic disorder that produces a variety of clinical neurological deficits, including psychomotor retardation, seizures and ataxia. The biochemical hallmark of l-2-HGA is the accumulation of l-2-hydroxyglutaric acid (l-2-HG) in cerebrospinal ...
L-2-Hydroxyglutaric acid disodium ((S)-2-Hydroxyglutaric acid disodium) 是一种表观遗传修饰因子,是肾癌中的表观遗传修饰剂和推定的癌代谢物,可用于肾癌的相关研究。它抑制线粒体肌酸激酶活性,Km 和 Ki 分别为 2.52 mM 和11.13 mM。它可抑制组蛋白去甲基化酶,从而促进组蛋白甲基化。
L-2-Hydroxyglutaric acid disodium 是一种表观遗传修饰因子,可用于肾癌的相关研究,也可抑制线粒体肌酸激酶 (Mi-CK) 活性。 产品性质 英文别名(English Synonym) L-2-Hydroxyglutaric acid disodium 中文名称(Chinese Name) / 靶点(Target) Histone Demethylase;Mitochondrial Metabolism Others ...
英文名称:2-hydroxyglutaric acid CAS:2889-31-8 纯度:97% HPLC 包装信息:1g;5g ChemeGen 中国 联系电话: 18818260767 产品介绍: 英文名称:α-Hydroxyglutaric Acid CAS:2889-31-8 纯度:98% 包装信息:10 mg;50 mg;100 mg;500 mg;1 g;5 g;10 g ...
Urinary 2-hydroxyglutaric acid was 1418 mmol/mol creatinine (controls <25). Analysis of the L-2-hydroxyglutarate dehydrogenase gene revealed a homozygous mutation in exon 2 (A320G). At the age of 20 years, an osteoma of the right frontal bone was diagnosed. This finding reinforces the ...
英文名L-α-Hydroxyglutaric acid disodium salt 中文别名L-2-羟基戊二酸二钠 英文别名更多 L-α-羟基戊二酸二钠盐生物活性 描述L-2-Hydroxyglutaric acid disodium 是一种表观遗传修饰因子,可用于肾癌治疗。L-2-Hydroxyglutaric acid disodium 可抑制组蛋白去甲基化酶 (histone demethylases),从而促进组蛋白甲基化...
L-2-羟基戊二酸二钠 英文别名: L-α-Hydroxyglutaric acid disodium salt; (2S)-2-Hydroxyglutaric Acid Disodium Salt 公司简介 郑州汇聚化工有限公司是集开发、生产、销售为一体的科技公司。公司拥有一批长期从事精细化学品开发和生产的 技术人员,以及设备齐全的研发实验室和中试车间。产品应用于全国各大院校、科研...
2H4]-D,L-2-羟基戊二酸性质、用途与生产工艺 生物活性 α-Hydroxyglutaric acid (2-Hydroxyglutarate) 是戊二酸的 α-羟基酸形式。α-Hydroxyglutaric acid 是多种 α-酮戊二酸依赖性双加氧酶 (包括 histone demethylases 和 5-甲基胞嘧啶羟化酶 (5-methlycytosine (5mC) hydroxylases) 的 TET 家族) 的...
CAS号:98891-36-2 Boc-L-homopropargylglycine CAS号:208522-16-1 L-Homopropargylglycine hydrochloride CAS号:942518-19-6 L-Arg-D-Ala-OH CAS号:55024-09-4 L-2-Hydroxyglutaric acid CAS号:13095-48-2 L-(3,3-2H2)Leucine CAS号:362049-59-0 ...
Chiral separation of 2-hydroxyglutaric acid on cinchonan carbamate based weak chiral anion exchangers by high-performance liquid chromatography. J. Chromatogr. A 1467, 239–245 (2016). Article PubMed CAS Google Scholar Fernández-Galán, E. et al. Validation of a routine gas chromatography mass...