Kikuchi–Fujimoto disease (KFD)是一种自限性疾病。镜下特点为副皮质区免疫母细胞增生,具有特征性核的组织细胞浸润,以及细胞凋亡或伴大量核碎片的坏死。 第五版WHO淋巴造血系统肿瘤分类中,将其列为T细胞为主的肿瘤样病变。 临床特点 ...
Kikuchi-Fujimoto病(Kikuchi-Fujimotodisease,KFD),又称组织细胞坏死性淋巴结炎(histiocytic necrotizing lymphadenitis,HNL)或亚急性坏死性淋巴结炎(subacutenecrotizing lymphadenitis,SNL),是一种良性、具有自限性特点,并且以颈部淋巴结肿大、长期低热、盗汗、白细胞减少为临床特点的...
Kikuchi-Fujimoto病(Kikuchi-Fujimoto disease,KFD)是一种自限性淋巴结病。镜下主要特点为副皮质区免疫母细胞增生,具有特征性核的组织细胞浸润,以及细胞凋亡或伴大量核碎片的坏死。 二、部位 淋巴结受累,极少数情况下会伴发皮肤病变。 三、临床特征 KFD在大部分患者中表现为急性或亚急性过程,病变常累犯单侧颈部淋巴...
Kikuchi-Fujimoto淋巴结炎(Kikuchi-Fujimoto disease, KFD),又称组织细胞坏死性淋巴结炎,是一种自限性疾病,以淋巴病变为特征,伴免疫母细胞副皮质区增生,具有特征性核特征的组织细胞浸润,伴大量核碎片的细胞凋亡或坏死。 ICD-O编码:无 ICD-11编码:4B2Y其他涉及免疫系统的特定疾病 相关术语 可接受的:组织细胞...
定义:组织细胞性坏死性淋巴结炎(Kikuchi-Fujimoto disease,KFD)是以淋巴结肿大为特征的病因不明的疾病,具有独特的组织学特征。 临床特征 1、发生率:不常见; 2、性别,种族和年龄分布:多为亚洲年轻女性(<40岁),但全世界都有报道; 3、危险因素:罕见情况下,严重的Kikuchi病例发生在免疫功能低下的患者中; ...
HutchinsonWangE.Kikuchi-fujimotodiseaseArchPatbol樊祥山摘译临床与实验病理学杂志
p pKikuchi-Fujimoto disease (KFD) is a benign and self-limited disorder, characterized by regional cervical lymphadenopathy with tenderness, usually accompanied with mild fever and night sweats. Less frequent symptoms include weight loss, nausea, vomiting, sore throat. Kikuchi-Fujimoto disease is an ...
Kikuchi-Fujimoto disease (KFD), also know as histiocytic necrotizing lymphadenitis, is a benign disorder characterized histologically by necrotic foci surrounded by histiocytic aggregates, and with the absence of neutrophils. KFD was recognized in Japan, where it was first described in 1972. The disea...
Kikuchi–Fujimoto disease (KFD)Juvenile idiopathic arthritis (JIA)Histiocytic necrotizing lymphadenitis or KikuchiFujimoto disease (KFD) is a rare, benign and self-limiting disorder that characteristically presents with fever and cervical lymphadenopathy. Articular manifestations in the form of arthralgias ...
Kikuchi-Fujimoto淋巴结炎(Kikuchi-Fujimoto disease, KFD),又称组织细胞坏死性淋巴结炎,是一种自限性疾病,以淋巴病变为特征,伴免疫母细胞副皮质区增生,具有特征性核特征的组织细胞浸润,伴大量核碎片的细胞凋亡或坏死。 ICD-O编码:无...