Mutations in PHKA2 are responsible for X-linked liver glycogen storage disease X-linked liver glycogenosis type I (XLG I) is due to a deficiency of phosphorylase kinase (PHK), a key enzyme in the control of glycogen breakdown. XLG I i... J Hendrickx,P Coucke,E Dams - 《American Journal...
Isolation and nucleotide sequence of human liver glycogen debranching enzyme mRNA: identification of multiple tissue-specific isoforms. Gene 1997; 197: 389-398Bao Y,Yang B,Lawson T, et al.Isolation and nucleotide sequence of human liver glycogen debranching enzyme mRNA:Identification of multiple ...
There were smaller ovaries and fewer follicles in the isolated rats. Fasting levels of liver glycogen were decreased in the males and of adrenal cholesterol in the females. Many of these changes indicate that hyperadrenocorticism is a consequence of prolonged isolation. 展开 ...
In 1976, Birnbaum and colleagues [3] adapted the technique of hepatocyte isolation for studies of hormone-stimulated glycogenolysis in goldfish cells. Since then, isolated fish hepatocytes have been used intensively in fresh suspensions and in primary culture as a powerful, yet simple tool for the...
- 《British Journal of Nutrition》 被引量: 119发表: 1997年 Effects of a submaximal treadmill training programme on histochemical properties, enzyme activities and glycogen utilisation of skeletal muscle in the horse SummaryThe effects of training on skeletal muscle composition were studied in four ...
- 《New England Journal of Medicine》 被引量: 737发表: 1993年 Chimerism after Liver Transplantation for Type IV Glycogen Storage Disease and Type 1 Gaucher's Disease. Background: Liver transplantation for type IV glycogen storage disease (branching-enzyme deficiency) results in the resorption of ...
A unit produces 1 nmol of β-naphthylamine per min under the standard assay conditions. Total glycogen phosphorylase was measured as described previously (34) in the presence of mM AMP. A unit of phosphorylase produces 1 nmol of inorganic phosphate per min. Protein Determination The protein ...
GLYCOGEN PHOSPHORYLASE INHIBITOR COMPOUND AND PHARMACEUTICAL COMPOSITION THEREOF This invention relates to a novel compound which is a glycogen phosphorylase inhibitor and its use in the treatment of diabetes and other conditions associated therewith. The invention further relates to a pharmaceutical compositio...
pseudotuberculosis appears as round, whitish, brilliant, and ‘slippery’ colonies, surrounded by a slight hemolysis zone), biochemical reactions (Catalase-positive, Urease-positive, Nitrate reductase-negative, indole-negative, H2S-negative, ferment glucose, maltose, mannose, fructose, and glycogen), ...
Figure 3. Primary hepatocytes subjected to PAS staining for glycogen (brightfield imaging). (A,B) Negative controls; (C,D) PAS staining of isolated cells. The isolated liver cells (cultured 6 days, passage 0) were assessed for hepatocyte-specific markers cytokeratin 18, AFP, and albumin usi...