[CV(%) = SD/mean x100].Storage Stability: The loss activity rate of this kit is less than 8% within the expiration date under appropriate storage condition.Cat.No: MBS
REFERENCESBattaileKP,etal.Structuresofisobutyryl-CoAdehydrogenaseandenzyme-productcomplex:comparisonwithisovaleryl-andshort-chainacyl-CoAdehydrogenases.JBiolChem.2004Apr16;279(16):16526-34.McePdfHeightCaution:Producthasnotbeenfullyvalidatedformedicalapplications.Forresearchuseonly.Tel:400-820-3792FaxE-mail:tech...
异丁酰辅酶A脱氢酶缺乏(Deficiency of isobutyryl-CoA dehydrogenase)基因检测就是线粒体基因检测吗? 是的,异丁酰辅酶A脱氢酶缺乏是一种线粒体基因突变导致的遗传疾病,因此基因检测可以通过检测线粒体基因来确定是否存在该疾病。异丁酰辅酶A脱氢酶缺乏(Deficiency of isobutyryl-CoA dehydrogenase)的有效治好性治疗会...
英文别名: ACAD8 (ARC42, IBD, Isobutyryl-CoA Dehydrogenase, Mitochondrial, Activator-recruited Cofactor 42kD Component, Acyl-CoA Dehydrogenase Family Member 8, ACAD-8, FLJ22590) (MaxLight 650)中文名: 中文别名: CBNumber: CB04959519 分子式: 分子量: 0 ...
BProblem statement:/B Human Isobutyryl-CoA Dehydrogenase (IBD) is member of the Acyl-CoA Dehydrogenases family. It is involved in Val metabolism. In this study we modified the purification method of the IBD and further spectroscopic characterization was conducted. BApproach:/B Using DTT in the ...
The electrons on reduced flavin are transferred to another flavoprotein, electron-transferring flavoprotein (ETF), which then transfers the reducing equivalents to membrane-bound ETF dehydrogenase, which reduces ubiquinone, a substrate of the respiratory chain.215 Most ACADs are dimers of dimers, with ...
<P>中文名称: Isobutyryl-CoA脱氢酶缺乏症</P><P>英文名称:Isobutyryl-Coa Dehydrogenase Deficiency </P><P>OMIM号: 611283 </P><P>所属系统:内分泌和代谢系统</P><P>遗传方式:AR</P><DIV class=hdwiki_tmml>疾病简介</DIV><P>患病者体内无法适当地代谢某些蛋白质。此酶的缺乏使缬氨酸代谢发生...
Structures of isobutyryl-CoA dehydrogenase and enzyme-product complex: comparison with isovaleryl- and short-chain acyl-CoA dehydrogenases. J Biol Chem 2004;279:16526-16534.Structures of isobutyryl-CoA dehydrogenase and enzyme-product complex: comparison with isovaleryl- and short-chain acyl-CoA ...
Isobutyryl-coenzyme_A_dehydrogenase_deficiencyIsobutyrylcoenzyme A dehydrogenase deficiencyInborn Errors of Metabolism
These results indicate that in the human, there is an isobutyryl-CoA dehydrogenase which exists as a separate enzyme serving only the valine pathway in addition to the 2-methyl branched-chain dehydrogenase which serves both the valine and the isoleucine pathways in both rat and human. Copyright ...