【疾病名】血友病甲 【英文名】hemophilia A 【缩写】 【别名】血友病 A 【ICD 号】D69.8 【概述】 血友病甲 (hemophilia A,HA)是一种X 染色体连锁的凝血因子Ⅷ量和分子 结构异常引起的隐性遗传性出血性疾病,临床特点为 “自发性”关节出血和深 部位组织出血。 早在公元 2 世纪,犹太法典已有类似血友病遗传...
We identified patients who received recombinant factor VIIa (rFVIIa), factor VIII inhibitor bypass activity (FEIBA), factor VIII or factor IX or had a diagnosis code for coagulation defects (ICD-9 286.xx). Use of antihemophilic drugs was identified through either pharmacy dispensing or provider ...