解析 是α-地中海贫血的中间型。是α0和α+地贫的杂合子状态。是由3个α珠蛋白基因缺失或缺陷所造成,患者仅能合成少量的α链,其多余的β链即合成HbH(β4)。其对氧亲和力高,是一种不稳定血红蛋白,容易在红细胞内变性沉淀而形成包涵体,造成红细胞膜僵硬而使红细胞寿命缩短。
人血红蛋白H(HbH)ELISA Kit 在线询价 进入商铺 同类产品 人血红蛋白H(HbH)ELISA Kit Human Hemoglobin H,HbH ELISA Kit发布时间:2025/3/15 10:19:35 关注度:1488 本试剂仅供研究使用 试剂盒组成: 试剂盒组成 48 孔配置 96 孔配置 保存 说明书 1 份 1 份 封板膜 2 片(48) 2 片(96) 密封袋 ...
Unused strips should be stored at 2-8掳C in their pouch with the desiccant provided.6) Use fresh disposable pipette tips for each transfer to avoid contamination.7) Do not mix acid and sodium hypochlorite solutions.8) Serum and plasma should be handled as potentially hazardous and capable of...
血红蛋白(Hemoglobin;Hb)(血红蛋白是什么意思?) 中文名称:血红蛋白英文名称:Hemoglobin化验介绍:血红蛋白是红细胞的主要成分。其功能是在肺部结合氧气,送到全身各组织并将组织中的二氧化碳送到肺部而呼出体外。临床意义:由于红细胞与血红蛋白有密切关系,因此它们的临床意义基本相同。但血红蛋白能好地反映贫血程度。正常参...
SynonymsHBH; ECYT7; HBA-T3; METHBA; hemoglobin subunit alpha 1 CategoryOthers Background血红蛋白由血红素和珠蛋白组成。血红蛋白的功能是将氧气从肺运送到组织。在成人中发现三种主要类型的正常血红蛋白:血红蛋白 A、血红蛋白 A2 和血红蛋白 F 即 alpha、beta、gamma 或 delta,决定了血红蛋白的类型。所有正常...
The clinical course of hemoglobin H (HbH) disease is remarkably variable. It is not completely clear how genetic and environmental factors interplay to mod... P Surapolchai,A Chuansumrit,N Sirachainan,... - 《Annals of Hematology》 被引量: 6发表: 2017年 A rare case of coinheritance of ...
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基因别名:HBA-T3; HBA1; HBA2; HBH UniProt ID:(Human) P69905 Entrez Gene ID:(Human) 3039 功能 peroxidase activityoxygen transporter activityiron ion bindingprotein bindingoxygen bindingheme bindinghaptoglobin binding 参与通路 receptor-mediated endocytosispositive regulation of cell deathoxygen transportbica...
HBH is a form of alpha-thalassemia due to the loss of three alpha genes. This results in high levels of a tetramer of four beta chains (hemoglobin H), causing a severe and life-threatening anemia. Untreated, most patients die in childhood or early adolescence. Similarity: Belongs to the ...
技术支持 货号MA5-35794 CNY4,839.00 100 µL 下单后预计有货时间 16-Apr-2025 查看价格 批量或定制请求 Application Created with Sketch. 图:1/7 Hemoglobin alpha Antibody (MA5-35794) in IHC (P) Immunohistochemistry analysis of Hemoglobin alpha in paraffin-embedded blood cell staining in human plac...