Remarkably, we also found that the frataxin-like protein Nqo15 from T. thermophilus complex I ameliorates the mitochondrial respiratory phenotype when expressed in FRDA patient's cells. Our data point to a structural and functional interaction of frataxin with complex I and open a perspective to ...
Therapeutic implications- Frataxin supplementation is being attempted either by direct delivery of frataxin protein (protein replacement therapy) (Britti et al., 2018; Vyas et al., 2012) or via delivery of a normal copy of the FXN gene via gene therapy (gene replacement therapy) (Gerard et ...
别称 CyaY, d-FXN, FA, FARR, Frataxin mature form, Frataxin(81-210), FRDA, FRDA_HUMAN, Friedreich ataxia protein, Fxn, i-FXN, m56-FXN, m78-FXN, m81-FXN, MGC57199, X25 菲恩生物蛋白表达平台,针对不同的蛋白性质与用途,专注解决各种困难蛋白的表达,纯化问题。我们拥有强大的技术团队,为您...
Frataxin/FXN Protein, Cynomolgus (His) MCE 国际站:Frataxin/FXN Protein, Cynomolgus (His) Synonyms: FXN; FRDA1; QnpA-13971; Frataxin; mitochondrial; Fxn; EC 1.16.3.1) [Cleaved into: Frataxin intermediate form; Frataxin mature form] Species: Cynomolgus Source: E. coli 蛋白编号:Q8HXX9 (S81...
MCE 国际站:Frataxin/FXN Protein, Human (His, Myc) 品牌:MedChemExpress (MCE) 货号:HY-P72266 纯度:Greater than 90% as determined by reducing SDS-PAGE. 运输条件:美国大陆的室温;其他地方可能有所不同。 产品活性:Frataxin/FXN 蛋白激活核心铁硫簇组装复合物,并加速 [2Fe-2S] 簇组装的硫转移。它在...
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An inherited deficiency in the frataxin protein causes neurodegeneration of the dorsal root ganglia and Friedreich's ataxia (FA). Frataxin deficiency leads to oxidative stress and inflammatory changes in cell and animal models; however, the cause of the inflammatory changes, and especially what causes...
Frataxin although stable 4C for 4 weeks, should be stored desiccated below -18C. For long term storage it is recommended to add a carrier protein (0.1% HSA or BSA). Please prevent freeze-thaw cycles. 其他 ProSpec 是一家全球著名细胞因子蛋白生产和研发的公司,具有20多年的生产经验,专注...
Immunogen Frataxin fusion protein Ag5316 种属同源性预测 Host / Isotype Rabbit / IgG Class Polyclonal Type Antibody Full Name frataxin Synonyms FXN, FA, Extramitochondrial frataxin, EC:1.16.3.1, dFXN Calculated Molecular Weight 23 kDa Observed Molecular Weight 14 kDa GenBank Accession Number BC0480...
Product Name:Frataxin Protein Quantity Dipstick Assay Kit Synonyms:Frataxin Protein Quantity Dipstick Assay Kit CAS: MF: MW:0 EINECS: Mol File:Mol File Information Error Report Your Email: Browse by NationalityFrataxin Protein Quantity Dipstick Assay KitSuppliersChina suppliers ...