This calcium association may becritical for protein-protein interactions and stabilization of the microfibrils.Mutations of the FBN1 gene have been shown to result in Marfan syndrome, a disease characterized by abnormal synthesis, secretion and matrix deposi-tion of fibrillin. FBN2 is also linked...
【纯化方法】:affinity purified by Protein A 【储存液】:0.01M PBS, pH 7.4 with 10 mg/ml BSA and 0.1% Sodium azide 【产品应用】:not yet tested in other applications.optimal dilutions/concentrations should be determined by the end user. ...
Protein | TwistDx | sigma aldrich | sigma | Life Technologies | Molecular Probes | gibco | invitrogen | thermo | Tonbo Biosciences | targetingsystems | sunrise sciene products | PEVIVA | MicroGEM | ModiQuest | LGC link | HILICON AB | Cellutron Life Technologies | Biomedical Research Service ...
Pathogenic variants affecting the TB5 domain of the fibrillin-1 protein: not only in geleophysic/acromicric dysplasias but also in Marfan syndrome doi:10.1136/jmg-2023-109646Genetic Diseases, InbornCardiovascular DiseasesMusculoskeletal DiseasesDiagnosisBackground Marfan syndrome (MFS) is a multisystem ...
Immunogen Fibrillin 1 fusion protein Ag30283 种属同源性预测 Host / Isotype Rabbit / IgG Class Recombinant Type Antibody Full Name fibrillin 1 Synonyms FBN1, MASS, Fibrillin-1, FBN, Asprosin Observed Molecular Weight 350 kDa GenBank Accession Number BC146854 Gene Symbol Fibrillin 1 Gene ID ...
Fibrillin 1 contains a large number of cysteine-rich epidermal growth factor (EGF)- like domains, most capable of binding calcium ions (cbEGF-like), and a few motifs homologous to the binding protein for transforming growth factor beta (TGFβ1-BP)- like module (PMID: 29220879, PMID: ...
AZFa protein DDX3Y is differentially expressed in human male germ cells during development and in testicular tumours: new evidence for phenotypic plasticity of germ cells. Hum Reprod. 2012;27(6):1547–55. 15. Lau SK, Weiss LM, Chu PG. TCL1 protein expression in testicular germ cell tumors....
MCE 国际站:Fibrillin-1/Asprosin Protein, Mouse (HEK293, His) Synonyms: rMuFibrillin-1/Asprosin, His; Fibrillin-1; Fbn1; Asprosin; Fbn-1 Species: Mouse Source: HEK 293 Biological Activity: Data is not available. 品牌介绍:• MCE (MedChemExpress) 拥有数百种全球独家化合物,我们致力于为全球...
RC-0625R ZNF268 (zinc finger protein ZNF268)- N-terminal (1a) 锌指脂蛋白-1a(抗原)RC-0626P ZNF268 (zinc finger protein ZNF268)- middle (1b) 锌指脂蛋白-1b(抗原)公司其他生化试剂产品有: M0014 胆固醇酯酶(猪胰)/胆甾醇酯酶(猪胰)/Cholesterol esterase 生物技术级,300u/mg 100u Amresco ...
Solid-phase and BIAcore binding studies showed that this fragment interacts strongly and specifically with N-terminal fibrillin-1, thereby inhibiting the association of C-terminal latent TGFbeta-binding protein 1 (a component of the large latent complex [LLC]) with N-terminal fibrillin-1. By ...