Cystic fibrosis is an inherited metabolic disorder, the chief symptom of which is a thick, sticky mucus that clogs the respiratory tract and the gastrointestinal tract. Cystic fibrosis is a recessive genetic disease that mainly affects persons of Europea
translucent lung fields, depressed or flattened diaphragm, right ventricular enlargement, areas of atelectasis and fibrosis. Arterial blood gas mild to moderate: acute alveolar hyperventilation with hypoxemiaSevere: chronic ventilatory failure with hypoxemia PFT decreased flowrates CBC elevated hb and HCT co...
Facilitates opening of the chloride channel ("CFTR Potentiator") • Indicated for patients aged > 1 month with an ivacaftor-responsive CFTR mutations Need 1 copy of F508 (heterozygous) 點擊卡片即可翻轉 👆 thekehealy22 Top creator on Quizlet ...
As part of the consultation you take a family history and draw the pedigree (family tree) (fig 1). Fig 1 Family tree 1. What does the double line between Mr and Mrs A represent? 2. You suspect an inherited disorder. Examining the pedigree, what is the most likely pattern of ...
Implications for nursing care are discussed.P. LomasS. FowlerAmerican Journal of NursingLomas, P. H., & Fowler, S. B. (2010). Parents and children with cystic fibrosis. American Journal of Nursing, 110(8), 30-37; quiz 38-39. doi: 10.1097/01.NAJ.0000387689.02005.1d...
107. The value of monitoring rint in children with cystic fibrosis over a course of intravenous antibiotic treatmentLondon Health Sciences Centre, London, Ontario.doi:10.1016/S0300-2977(99)90159-6L. MorrisonJ. LangleyS.P. ConwayK.G. Brownlee...
Prevalence of non-tuberculous mycobacteria (NTM) in pediatric patients with cystic fibrosis (CF) in Florida – A two center studyAsthma is a chronic disorder of the airways characterized by variable and recurring symptoms of cough, wheezing and chest tightness, airflow obstruction, bronchial ...
Preconception and prenatal screening for cystic fibrosis. MLO: medical laboratory observer. 2002; 34:8-12.Baskin LB, Wians FH Jr, Elder F. Preconception and prenatal screening for cystic fibrosis. MLO: medical laboratory observer. 2002; 34:8-12. quiz 4, 6. [PubMed: 12385171]...
Pediatric Nursing 36: 284-291.O'Haver J, Moore IM, Insel KC, Reed PG, Melnyk BM, Lavoie M. Parental perceptions of risk and protective factors associated with the adaptation of siblings of children with cystic fibrosis. Pediatr Nurs 2010 Nov-Dec;36(6):284-91; quiz 292....
13. The parents of an infant diagnosed with cystic fibrosis ask the nurse to define cystic fibrosis for them. Which response by the nurse is accurate? "Cystic fibrosis is an autosomal recessive disorder that affects the infant's lungs, pancreas, and intestines." 14. A newborn infa...