translucent lung fields, depressed or flattened diaphragm, right ventricular enlargement, areas of atelectasis and fibrosis. Arterial blood gas mild to moderate: acute alveolar hyperventilation with hypoxemiaSevere: chronic ventilatory failure with hypoxemia PFT decreased flowrates CBC elevated hb and HCT co...
Dosing should be interrupted if the ALT or AST concentrations are more than 5X the upper limit of normal or if ALT or AST is greater than 3X the upper limit of normal with bilirubin > 2X the upper limit of normal Ivacaftor Summary
The parents of a child with cystic fibrosis tell the nurse they are considering having more children and want to know the likelihood of having another child with cystic fibrosis. Which response by the nurse is appropriate? "Since cystic fibrosis is an autosomal recessive trait, your chil...
Later on: HTN, cardiac hypertrophy, CHF, renal failure, hepatic fibrosis; Ultrasound: large kidneys w/ no macrocysts; 50% early mortality due to renal failure and pulmonary hypoplasia, but much better survival after first year; Tx: respiratory assistance, nephrectomy, antihypertensives, treat hepat...