Cystic fibrosis–related diabetes is becoming more common as patients live longer. Children with cystic fibrosis have a high incidence of tooth discoloration when systemic tetracyclines are taken during tooth formation. With the advent of alternative antibiotics the incidence of tooth discoloration is ...
Abbreviations: HR: hazard ratio; CFTR: cystic fibrosis transmembrane conductance regulator; CFRD: cystic fibrosis related diabetes; CFLD: cystic fibrosis related liver disease Young pwCF with CFLD had an increased risk of Pa-IA (HR 1.30; 95% CI: 0.98–1.73). The risk was unchanged for Pa-CC...
Adult bronchiectasis was defined by the following criteria: (1) age ≥ 20 years; (2) with at least one claim under the International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10) code J47; and (3) excluding those with cystic fibrosis (ICD-10 diag...
Liver disease, which included hepatomegaly, liver cysts, Caroli disease, congenital hepatic fibrosis, and signs of portal hypertension was assessed on abdominal US and, if indicated, on MRI scans. In selected patients with high suspicion who did not meet the above-mentioned clinical criteria, the...