The congenital long QT syndrome (LQTS) is considered to be one of the hereditary cardiac arrhythmia syndromes, nowadays also known as cardiac channelopathies. The syndrome is characterized by prolongation of the heart rate corrected QT-interval (QTc) on the 12-lead electrocardiogram (ECG). In ...
Congenital long QT syndrome (LQTS) is a hereditary cardiac disease characterized by a prolongation of the QT interval at basal ECG and by a high risk of life-threatening arrhythmias. Disease prevalence is estimated at close to 1 in 2,500 live births. The two cardinal manifestations of LQTS ...
长QT综合征(long QT syndrome, LQTS)是一种心室肌复极异常,特征为心电图上QT间期延长 (波形1),可导致有症状的室性心律失常和心脏性猝死(sudden cardiac death, SCD)风险增加[1]。LQTS患者的主要症状包括晕厥、癫痫发作、心搏骤停(sudden cardiac arrest, SCA)和SCD。该综合征与一种危及生命的特征性心律失常风险...
For the long-QT syndrome (LQTS), figures ranging from 1: 20 000 to 1: 5000 were published, but none was based on actual data. Our objective was to define the prevalence of LQTS. \udMethods and Results-In 18 maternity hospitals, an ECG was performed in 44 596 infants 15 to 25 days...
the QRS complex or the QT interval, reflect atrial and ventricular depolarization or repolarization and can be measured by surface electrocardiography (ECG). Thus, any changes in ECG intervals can indicate abnormalities in cardiac conduction or electrical instability of the heart muscle leading to cardi...
This would include conditions such as Marfan syndrome, many of the cardiomyopathies, and the inherited arrhythmias such as long QT or catecholaminergic polymorphic ventricular tachycardia. Evaluation during pregnancy Symptoms that arise d...
多基因突变: CATCH-22 Syndrome :22q11 3. 单基因缺陷: Noonan Syndr. (PS), Holt-Oram Syndr.( ASD); Long QT Syndr., Marfan Syndr. 8% 外因和环境因素(Environmental Aspects) 宫内感染 — 风疹综合征、腮腺炎、柯萨基病毒等 放射线 药物影响 — 抗癌药、抗癫痫药、抗心律失常药物 营养缺乏 — ...
Taking into account the risk of TdP, it is reasonable to consider takotsubo cardiomyopathy as a potential cause of acquired long QT syndrome. 展开 关键词: Takotsubo Stress-related cardiomyopathy QT prolongation Torsade de pointes Atrioventricular block DOI: 10.1007/s00059-013-3756-8 被引量: 2...
The subcutaneous implantable cardioverter defibrillator (S-ICD) provides an attractive option for patients with congenital heart disease (CHD) in whom a transvenous defibrillator is contraindicated. Given the unusual cardiac anatomy and repolarization strain, the surface electrocardiogram (ECG) is frequently...
Deafness is genetically very heterogeneous and forms part of several syndromes. So far, delayed rectifier potassium channels have been linked to human deafness associated with prolongation of the QT interval on electrocardiograms and ventricular arrhythmia in Jervell and Lange-Nielsen syndrome. Cav1.3 volt...