Under the same conditions, lignoceric acid beta-oxidation was impaired in the above three peroxisomal disease states. These results provide evidence that branched chain fatty acid, as well as very long chain fatty acid, beta-oxidation occurs only in peroxisomes. As the defect in X-linked ALD is...
In the animal studies, changes in isobutyric and isovaleric acid were the most striking as their content was not only driven by HFHS diet but also by the PM and by their interaction (Fig.3l–m). Moreover, the production of these BCFA and that of their hepatic oxidation intermediates was ...
The relationship between odd- and branched-chain fatty acids and microbial nucleic acid bases in rumen (1950) The fate of branched chain fatty acids in animal body IV. The biological significance of [omega]-oxidation of fatty acids More results ► Dictionary browser ? ▲ Brampton bran bran fl...
In contrast to 3-methyl-butyric acid (isovaleric acid), 3-methylvaleric acid can be catabolized by an initial α-oxidation. This reaction sequence demonstrates that alternations between α- and /gb-oxidations can take place in the degradation of a branched chain fatty acid....
Phytanic acid (3,7,11,15-tetramethylhexadecanoic acid) is a branched-chain fatty acid derived from dietary sources and broken down in the peroxisome to pristanic acid (2,6,10,14-tetramethylpentadecanoic acid) via alpha-oxidation. Pristanic acid then undergoes beta-oxidation in peroxisomes. Phyt...
The in vitro omega-oxidation of phytanic acid and other branched chain fatty acids by mammalian liver . Scand. J. Clin. Lab. Invest. 22 : 224–230Try K. (1968) The in vitro omega-oxidation of phytanic acid and other branched chain fatty acids by mammalian liver. Scand. J. Clin. Lab...
1990. Effect of infused branched-chain amino acids on muscle and whole-body amino acid metabolism in man. Cli. Sci. (Lond.). 79:457-466... Louard, Rita J,Barrett, Eugene J,Gelfand, Robert A - 《Clinical Science》 被引量: 403发表: 1990年 Leucine oxidation in diabetes and starvation...
A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders J. Lipid Res., 31 (1990), pp. 217-225 View PDFView articleView in ScopusGoogle Scholar 9 G. Vanhove, P.P. Van Veldhoven, F. Vanhoutte, G. Parmentier...
U. et al.α-ketoisocaproic acid and leucine provoke mitochondrial bioenergetic dysfunction in rat brain. Brain Res. 1324, 75–84 (2010). CAS PubMed Google Scholar Adams, S. H. et al. Plasma acylcarnitine profiles suggest incomplete long-chain fatty acid β-oxidation and altered ...
www.nature.com/scientificreports OPEN received: 24 March 2016 accepted: 16 August 2016 Published: 06 September 2016 Xanthomonas campestris FabH is required for branched-chain fatty acid and DSF-family quorum sensing signal biosynthesis Yong-Hong Yu1,2, Zhe Hu1, Hui-Juan Dong1, Jin-...