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尾-Mannosidosis, an inherited glycoprotein metabolic disorder so far identified only in the caprine species, is characterized by deficiency of 尾-mannosidase, oligosaccharide accumulation and excretion, neurovisceral cytoplasmic lysosomal storage vacuoles and central nervous system myelin and axonal lesions....
A big step towards routine: The title synthesis provides mannuronic acid alginate fragments featuring up to 12 cis-mannosidic linkages, in multi-milligram quantities (see scheme; Bn=benzyl, Lev=levulinoyl). Mannuronic acid building blocks were used in a second-generation carbohydrate synthesizer ...
网络甘露糖苷贮积症 网络释义 1. 甘露糖苷贮积症 [91]. β-甘露糖苷贮积症(beta-Mannosidosis)[92]. 半乳糖唾液酸苷贮积症(Galactosialidosis, several forms)神经系统罕见疾 … blog.sina.com.cn|基于 1 个网页
Caprine beta-mannosidosis is an inherited lysosomal storage disorder due to a deficiency of beta-mannosidase which cleaves beta-linked mannose residues from the ends of N-asparagine linked oligosaccharides of glycoproteins. Histological and chemical examination has revealed a deficiency of compact myelin...
Rheumatoid arthritisM2000Mannuronic acidDMARDTh17 cellsIL-17This study aimed at investigating the inhibitory edoi:10.1007/s10787-017-0410-8AhmadiUnivHosseinUnivMahmoudiUnivMahdiUnivGharibdoostUnivFarhadUnivVojdanianUnivJamshidiUnivAhmadUnivRezaUnivInflammopharmacology...
I HOSIEPO Box 377, Atherton, Queensland 4883T STAPLETONPorter Street, Wyong, New South Wales 2239John Wiley & Sons, LtdAustralian Veterinary JournalHealy PJ, Kidd GN, Reuter RE et al. b-mannosidosis in Salers calves in Australia. Aust Vet J 1992;69:145....
Zamet (1992) Human beta-mannosidosis: a 3-year-old boy with speech impairment and emotional instability. Clin. Genet. 41: 331–340.Poenaru L, Akli S, Rocchiccioli F, Eydoux P, Zamet P: Human beta- mannosidosis: a 3-year-old boy with speech impairment and emotional instability. ...
The clinical features of caprine beta-mannosidosis were evaluated in 10 newborn goats, one stillborn goat and one goat fetus. The phenotypic abnormalities observed in all 10 live affected animals included an inability to rise from a recumbent position, moderate to marked intention tremor, eye ...
The beta- mannuronic acid oligosaccharides can be conjugated to carriers and used to generate antibodies against Pseudomonas aeruginosa.OVERKLEEFT, Herman StevenVAN DER ELST, HansVAN DER MAREL, Gijsbert, ArieWALVOORT, Maria Theresia CorneliaCODEE, Jeroen Dirk Cornelis...