Pulmonary hypertension is a life-threatening condition that gets worse over time, but treatments can help your symptoms so you can live better with the disease. It may take some planning, but plenty of people who have it find ways to do all the things they love, just as they did before ...
Advances in treatment have improved quality of life and survival, but life expectancy for those with moderate to advanced symptoms is relatively poor and response to treatments is very unpredictable. The mean survival has improved from about two years to over six to seven years. Whether medical ...
Primary pulmonary hypertension (PPH) is a rare disease characterized by elevated pulmonary artery pressure with no apparent cause. PPH is also termed precapillary pulmonary hypertension or, more recently, idiopathic pulmonary arterial hypertension (IPAH)
34]. Prospective hemodynamic studies have shown that 2-6% of patients with portal hypertension had PH [35,36]. However, RHC is mandatory for the diagnosis of portal PH, as several mechanisms may increase pulmonary artery pressure in the setting...
Pulmonary arterial hypertension (PAH) is tough to diagnose. Its symptoms can mimic other, less serious conditions. Your doctor will most likely try to rule out other causes of your symptoms first. You may need to see a heart specialist, called a cardiologist, or a lung specialist, called a...
This condition is manifest by clinical symptoms including dyspnea, fatigue, and chest pain along with signs of elevated pulmonary pressures and right heart dysfunction. The clinical evaluation of pulmonary hypertension includes numerous invasive and noninvasive testing including blood work, imaging ...
Pulmonary arterial hypertension (PAH) is a multifactorial disease associated with the remodeling of pulmonary blood vessels. If left unaddressed, PAH can lead to right heart failure and even death. Multiple biological processes, such as smooth muscle pro
In summary, the patient received a diagnosis of idiopathic pulmonary arterial hypertension (IPAH). According to the 2022 ESC/ERS guidelines, she can be classified as WHO functional class 3 symptoms requiring double-combination therapy based on endothelin receptor antagonists, phosphodiesterase-5 inhibitor...
PAH is defined by a persistent elevation in pulmonary artery pressure with normal left-sided pressures, differentiating it from left-sided heart disease. Symptoms progress from shortness of breath and decreasing exercise tolerance to right heart failure, with peripheral edema and marked functional ...
PAH diagnosis is based on right heart catheterisation (RHC) [1], showing a mean pulmonary arterial pressure (mPAP) above 25 mmHg, associated with pulmonary capillary wedge pressure (PCWP) under 15 mmHg, in favour of pre-capillary pulmonary hypertension (PH). To confirm PAH, other aetiologies...