He had significant proteinuria with renal and bone marrow biopsies confirming light-chain amyloidosis. Cardiac magnetic resonance imaging revealed concentric left-ventricular hypertrophy with an ejection fraction of 65%, left-ventricular end-diastolic volume of 146 mL, left-ventricular end-systolic volume ...
Amyloidosis⁎ Sarcoidosis⁎ Gaucher's disease Hurler's disease Fatty infiltration Storage diseases Hemochromatosis Fabry's disease Glycogen storage disease Endomyocardial Endomyocardial fibrosis⁎ Hypereosinophilic syndrome Carcinoid heart disease Metastatic cancers Radiation⁎ Toxic effects of anthracycline⁎...
Among patients with LV hypertrophy caused by cardiac amyloidosis, it has been reported that approximately 70% demonstrate a pattern of global subendocardial gadolinium enhancement, a pattern of enhancement not usually seen in patients with HCM (190). These data suggest that gadolinium-enhanced CMR ...
: A report of the American College of Cardiology/American Heart Association Task Force on assessment of diagnostic and therapeutic cardiovascular procedures (subcommittee to develop guidelines for the clinical application of echocardiography) Author links open overlay panelChairman Gordon A. Ewy MD, FACC...
In addition, AF may be associated with HCM, dilated cardiomyopathy, or congenital heart disease, especially atrial septal defect in adults. Potential etiologies also include restrictive cardiomyopathies (e.g., amyloidosis, hemochromatosis, and endomyocardial fibrosis), cardiac tumors, and constrictive ...
Evidence in the literature about an association between COVID-19 and neurodegeneration is unclear. For the most part, at least clinically, cases were confirmed from the standpoint of acuity to have been the result of COVID-19, but there is no definite biochemical evidence of such a correlation...
Strain and strain rate values have been studied in a number of conditions affecting the right heart, including arrhythmogenic RV dysplasia,131 pulmonary embolism,132 PH,133 systemic right ventricle,134 and amyloidosis.135, 136, 137 There is a lack of normative data for strain and strain rate mea...
Cardiac amyloidosis, glycogen-storage diseases, Anderson-Fabry disease, and Freiderich’s ataxia can all cause hypertrophy but usually have concomitant noncardiac signs and symptoms that help steer the clinician toward the systemic disease process, including abnormally elevated creatine kinase, pre...
59 - An elusive diagnosis: cardiac amyloidosis H Malik, A Malik, LS Engel, S Sanne, S Vignes Page S35 View PDF select article 60 - Biventricular thrombi in young female with non-ischemic cardiomyopathy Conference abstractFull text access 60 - Biventricular thrombi in young female with non-...
Prognostic and Added Value of Two-Dimensional Global Longitudinal Strain for Prediction of Survival in Patients with Light Chain Amyloidosis Undergoing Autologous Hematopoietic Cell Transplantation Pun, Shawn C.Landau, Heather J.Riedel, Elyn R.Jordan, JonathanYu, Anthony F.Hassoun, HaniChen, Carol L...