23 alpha-galactosidase: purification and substrate specificity.Carbohydrate Polymers. 2001L. D. Varbanets, V. M. Malanchuk, T. T. Buglova, and R. A. Kuhlmann, "Penicillium sp. 23 alpha-galactosidase: purification and substrate specificity," Carbohydrate Polymers, vol. 44, no. 4, pp. 357...
样本:Alpha-galactosidase A ELISA Kit 检测方法:详见说明书 应用:ELISA 检测限:0.156-10 ng/mL 货号:BK-F100302 是否进口:是 ELISA试剂盒实验原理: ELISA是以免疫学反应为基础,将抗原、牽9体的特异性反应与酶对底物的高效催化作用相结合起来的一种敏感性很高的试验技术。由于抗原、抗体的反应在一种固相载体──...
Alpha 2,3-ST 1; CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 1; DKFZp666E036; DKFZp779K2051; EC 2.4.99; EC 2.4.99.4; Gal-beta-1,3-GalNAc-alpha-2,3-sialyltransferase; Gal-NAc6S; sialyltransferase 4A (beta-galactosidase alpha-2,3-sialytransferase); sia...
Safety and efficacy of recombinant human alpha-galactosidase A--replacement therapy in Fabry's disease. BACKGROUND: Fabry's disease, lysosomal alpha-galactosidase A deficiency, results from the progressive accumulation of globotriaosylceramide and related gly......
nalfa;— fetoproteinalfa fetoproteína;— galactosidasealfa galactosidasa;— hydroxy acidsácidos alfa hidróxidos;— methyldopaalfa metildopa English-Spanish/Spanish-English Medical Dictionary Copyright © 2006 by The McGraw-Hill Companies, Inc. All rights reserved. ...
Speaket al., 2007). Recently, SAP-B−/−mice were described to accumulate Gb3 in various tissues, which is in agreement with previous findings that SAP-B is required to activate the degradation of Gb3 by α-galactosidase A (Sunet al., 2008). Sinceglobosidesand isoglobosides use the ...
GLAa Xq22 Alpha- galactosidase A Fabry's disease FXN 9q13 Frataxin Friedrich's ataxia PTPN11b 12q24.1 Protein tyrosine phosphatase, non-receptor type 11 Noonan's syndrome Note: In patients with cardiac hypertrophy secondary to Noonan's syndrome, PTPN11 mutations are quite uncommon (<10%) ...
1D). Treating adipocyte enriched membrane proteins with an alpha-exogalactosidase (alpha1–3,6) followed by analysis of released N-glycans by PGC-LC-MS/MS resulted in a significant reduction in the core-fucosylated non-sialylated di-hexose containing N-glycans, HexNAc4Hex6Fuc1 and HexNAc4Hex...
motif on the protein. Thus, the assay provides the option of either direct analysis of the motif on a glycoprotein of interest or measurement of the disaccharide following release by, for example, the enzyme endo-beta-galactosidase C fromClostridium perfringens....
In previous studies, a cyanogen bromide peptide derived from amino-acid residues 3-92 of beta-galactosidase (EC 3.2.1.23; beta-D-galactoside galactohydrolase) was shown to have alpha-donor activity in intracistronic alpha-complementation. We have now isolated the defective beta-galactosidase alpha-...