Deficiency: Level <1.5 g/L (<20 umol/L) VI. Management See COPD Management Eliminate exacerbating exposures Avoid Tobacco exposure Avoid occupational exposures of airborne toxins Substitution therapy with human Alpha-1 Antitrypsin (Aralastin, Prolastin) Weekly injection of Alpha-1 Antitrypsin (60 ...
Alpha‐1‐antitrypsinZ variantChronic obstructive pulmonary diseaseLiver diseaseLaboratory testingAlpha(1)-antitrypsin deficiency is characterized by a pathologic reduction of the serum concentration of alpha(1)-antitrypsin, the most important antiprotease in . It is one of the most common in Caucasians...
Alpha-1 antitrypsin(抗胰蛋白酶) deficiency is a genetic disorder(遗传病) in which a protein called alpha-1 antitrypsin is defective or absent, and it causes lung and liver disease. α抗胰蛋白酶缺乏症是一种遗传性疾病,患者体内的一种叫做α抗胰蛋白酶的蛋白质出现了问题或者含量减少了,最终导致肺...
Alpha-1-antitrypsin deficiency (AATD) is a rare genetic disorder associated with the development of liver and lung disease. AAT is a 52-kD glycoprotein, produced mainly by hepatocytes and secreted into the blood. Agglomeration of the AAT-protein in hepatocytes can result in liver disease. Exposur...
Alpha-1 antitrypsin(抗胰蛋白酶)deficiency is a genetic disorder(遗传病)in which a protein called alpha-1antitrypsin is defective or absent, and it causes lung and liver disease. α抗胰蛋白酶缺乏症是一种遗传性疾病,患者体内的一种叫做α抗胰蛋白酶的蛋白质出现了问题或者含量减少了,最终导致肺和肝脏...
Alpha-1抗胰蛋白酶缺乏症的英文名字是Alpha-1 antitrypsin deficiency。基因解码表明:Alpha-1抗胰蛋白酶缺乏症是一种遗传性疾病,与基因突变密切相关。Alpha-1抗胰蛋白酶是一种由SERPINA1基因编码的蛋白质,它在肝脏中合成并通过血液循环分布到全身。该蛋白质的主要功能是
英文: Metabolic diseases such as Wilson\'s disease, hemochromatosis, and alpha 1 - antitrypsin deficiency can lead to liver damage.中文: 代谢性疾病,如威尔逊氏病,血色沉着,α-1型胰岛素缺乏症均可导致肝损伤。英文: Alpha 1-antitrypsin Matrix Attachment Region Enhances RNA PolymeraseⅡ-dependent ...
Alpha-1-antitrypsin augmentation therapy for alpha-1-antitrypsin deficiency Alpha-1-antitrypsin (A1AT) deficiency is a genetic disorder characterized by low serum levels of A1AT and a high risk for the development of emphysema. A1A... Richard,C.,Hubbard,... - 《American Journal of Medicine》...
doi:10.1080/21548331.1971.11706032HarveyUniversityL.UniversitySharpUniversityInformaworldHospital PracticeSharp H. L. Alpha-1-antitrypsin deficiency. Hosp Pract 1971 ; 6: 83 [Taylor & Francis Online]
genetic model of alpha-1-antitrypsin deficiency. chinese.eurekalert.org 圣路易大学儿童医学系塔克曼博士(Jeffrey Teckma)所领导的研究团队,证实了甲一型胰蛋白酵素抑 制剂 缺陷 动 物模 式中有氧化压力的产生。 chinese.eurekalert.org [...] and registered as having originated from the Liberian Camp ...